D74.0
BillableCongenital methemoglobinemia
Congenital methemoglobinemia
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Congenital NADH-methemoglobin reductase deficiency
- Hemoglobin-M [Hb-M] disease
- Methemoglobinemia, hereditary
Excludes 2
Conditions not included here, but the patient may have both
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Also Known As / Clinical Terms
SNOMED CT
- Haemoglobin M disease74912001
- Hemoglobin M disease74912001
- Hereditary M haemoglobinopathy74912001
- Hereditary M hemoglobinopathy74912001
- Hereditary methaemoglobinuria74912001
- Hereditary methemoglobinaemia due to globin chain mutation74912001
- Hereditary methemoglobinemia due to globin chain mutation74912001
- Hereditary methemoglobinuria74912001
- Congenital methaemoglobinaema with defective methaemoglobin-reducing system234395000
- Congenital methemoglobinaema with defective methemoglobin-reducing system234395000
- Congenital methaemoglobinaemia with abnormal methaemoglobins234396004
- Congenital methemoglobinemia with abnormal methemoglobins234396004
- Congenital methaemoglobinaemia267550008
- Congenital methemoglobinemia267550008
- Hereditary methemoglobinaemia267550008
- Hereditary methemoglobinemia267550008
- Autosomal recessive congenital methaemoglobinaemia767497003
- Autosomal recessive congenital methemoglobinemia767497003
- Chronic familial methaemoglobin reductase deficiency767497003
- Chronic familial methemoglobin reductase deficiency767497003
- Congenital NADH-methaemoglobin reductase deficiency767497003
- Congenital NADH-methemoglobin reductase deficiency767497003
- Congenital methaemoglobinaemia due to NADH-cytochrome b5 reductase 3 deficiency767497003
- Congenital methemoglobinemia due to NADH-cytochrome b5 reductase 3 deficiency767497003
- Cytochrome b5 reductase deficiency767497003
- NADH-methaemoglobin reductase deficiency767497003
- NADH-methemoglobin reductase deficiency767497003
- Autosomal recessive congenital methaemoglobinaemia type II767498008
- Autosomal recessive congenital methemoglobinemia type II767498008
- Autosomal recessive congenital methaemoglobinaemia type I767499000
- Autosomal recessive congenital methemoglobinemia type I767499000
UMLS
- Autosomal recessive congenital methaemoglobinaemiaC0268193
- Autosomal recessive congenital methemoglobinemiaC0268193
- Autosomal recessive congenital methemoglobinemia (disorder)C0268193
- Chronic familial methaemoglobin reductase deficiencyC0268193
- Chronic familial methemoglobin reductase deficiencyC0268193
- Congenital NADH-methaemoglobin reductase deficiencyC0268193
- Congenital NADH-methemoglobin reductase deficiencyC0268193
- Congenital methaemoglobinaemia due to NADH-cytochrome b5 reductase 3 deficiencyC0268193
- Congenital methemoglobinemia due to NADH-cytochrome b5 reductase 3 deficiencyC0268193
- Cytochrome b5 reductase deficiencyC0268193
- DIHYDROLIPOAMIDE DEHYDROGENASE DEFICIENCYC0268193
- Deficiency of cytochrome-b5 reductaseC0268193
- Deficiency of cytochrome-b5 reductase (disorder)C0268193
- Deficiency of cytochrome-b<sub>5</sub> reductaseC0268193
- Deficiency of cytochrome-b<sub>5</sub> reductase (disorder)C0268193
- Deficiency of cytochrome-b>5< reductaseC0268193
- Deficiency of cytochrome-b>5< reductase (disorder)C0268193
- Diaphorase deficiencyC0268193
- Methemoglobinemia due to deficiency of methemoglobin reductaseC0268193
- Methemoglobinemia, Congenital, Autosomal RecessiveC0268193
- NADH cytochrome B5 reductase deficiencyC0268193
- NADH cytochrome b5 reductase deficiencyC0268193
- NADH diaphorase deficiencyC0268193
- NADH methemoglobin reductase deficiencyC0268193
- NADH-CYB5R deficiencyC0268193
- NADH-cytochrome b5 reductase deficiencyC0268193
- NADH-dependent methemoglobin reductase deficiencyC0268193
- NADH-methaemoglobin reductase deficiencyC0268193
- NADH-methemoglobin reductase deficiencyC0268193
- Nadh-Cytochrome B5 Reductase DeficiencyC0268193
- Congenital MethemoglobinemiaC0272087
- Congenital methaemoglobinaemiaC0272087
- Congenital methemoglobinemiaC0272087
- Congenital methemoglobinemia (disorder)C0272087
- Hereditary methemoglobinaemiaC0272087
- Hereditary methemoglobinemiaC0272087
- congenital methemoglobinemiaC0272087
- hemoglobin m diseaseC0272087
- hereditary methemoglobinemiaC0272087
- Haemoglobin M diseaseC3665425
- Hemoglobin M DiseaseC3665425
- Hemoglobin M diseaseC3665425
- Hereditary M haemoglobinopathyC3665425
- Hereditary M hemoglobinopathyC3665425
- Hereditary methaemoglobinuriaC3665425
- Hereditary methemoglobinaemia due to globin chain mutationC3665425
- Hereditary methemoglobinemia due to globin chain mutationC3665425
- Hereditary methemoglobinemia due to globin chain mutation (disorder)C3665425
- Hereditary methemoglobinuriaC3665425
- Methemoglobinemia, hereditaryC3665425
- Hemoglobin-M [Hb-M] diseaseC2873821
Frequently Asked Questions
What is ICD-10 code D74.0?
ICD-10-CM code D74.0 represents "Congenital methemoglobinemia". It is a billable/specific code that can be used on a claim.
Is D74.0 a billable code?
Yes, D74.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D74.0 in?
D74.0 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What SNOMED CT codes does D74.0 map to?
D74.0 maps to 7 SNOMED CT concepts: 767497003, 767499000, 767498008, 234395000, 267550008, and 2 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D74.0?
D74.0 is linked to 4 UMLS Concept Unique Identifiers: C0268193, C0272087, C3665425, C2873821. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.