D68.2
BillableHereditary deficiency of other clotting factors
Hereditary deficiency of other clotting factors
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- AC globulin deficiency
- Congenital afibrinogenemia
- Deficiency of factor I [fibrinogen]
- Deficiency of factor II [prothrombin]
- Deficiency of factor V [labile]
- Deficiency of factor VII [stable]
- Deficiency of factor X [Stuart-Prower]
- Deficiency of factor XII [Hageman]
- Deficiency of factor XIII [fibrin stabilizing]
- Dysfibrinogenemia (congenital)
- Hypoproconvertinemia
- Owren's disease
- Proaccelerin deficiency
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- abnormal coagulation profile NOS (R79.1)
Excludes 2
Conditions not included here, but the patient may have both
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
- coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
Also Known As / Clinical Terms
SNOMED CT
- Factor V deficiency4320005
- Factor XIII inhibitor disorder13993001
- Drug-induced coagulation inhibitor disorder16773005
- Factor XIII deficiency18604004
- Factor XIII deficiency disease18604004
- Fibrin stabilising factor deficiency18604004
- Fibrin stabilizing factor deficiency18604004
- Acquired neonatal factor II deficiency disease24149006
- Haemorrhagic disease of the newborn due to factor II deficiency24149006
- Hemorrhagic disease of the newborn due to factor II deficiency24149006
- Fitzgerald factor deficiency27312002
- Fitzgerald-Flaujeac-Williams-Reid trait27312002
- High molecular weight kininogen deficiency27312002
- Congenital fibrinogen deficiency31925001
- Hereditary factor I deficiency disease31925001
- Hereditary hypofibrinogenaemia31925001
- Hereditary hypofibrinogenemia31925001
- Hereditary factor II deficiency disease33297000
- Hereditary hypoprothrombinaemia33297000
- Hereditary hypoprothrombinemia33297000
- Deficiency of stable factor37193007
- F7 - Factor VII deficiency37193007
- Factor 7 deficiency37193007
- Factor VII deficiency37193007
- Prothrombin conversion accelerator deficiency37193007
- Stable factor deficiency37193007
- Hereditary Stuart factor deficiency disease37350004
- Hereditary Stuart-Prower deficiency disease37350004
- Hereditary factor X deficiency disease37350004
- Hereditary factor VII deficiency disease40855001
- Hereditary factor VII deficiency syndrome40855001
- Hereditary hypoproconvertinaemia40855001
- Hereditary hypoproconvertinemia40855001
- Hereditary Hageman factor deficiency disease43217004
- Hereditary factor XII deficiency disease43217004
- Platelet procoagulant activity deficiency43346008
- Congenital dysfibrinogenaemia45366001
- Congenital dysfibrinogenemia45366001
- Hereditary dysfibrinogenaemia45366001
- Hereditary dysfibrinogenemia45366001
- Factor XII deficiency46981006
- Factor XII deficiency disease46981006
- Hageman factor deficiency46981006
- Fletcher factor deficiency48976006
- Fletcher trait48976006
- Prekallikrein deficiency48976006
- Hereditary factor XIII deficiency disease50189006
- Laki-Lorand factor deficiency disease50189006
- Acquired anticoagulants64509006
- Acquired coagulation factor inhibitor disorder64509006
- Circulating anticoagulant disorder64509006
- Factor II deficiency73975000
- Prothrombin deficiency73975000
- Factor 10 deficiency76642003
- Factor X deficiency76642003
- Stuart-Prower factor deficiency76642003
- AC globulin deficiency88776002
- Hereditary factor V deficiency disease88776002
- Hereditary hypoproaccelerinaemia88776002
- Hereditary hypoproaccelerinemia88776002
- Owren's disease88776002
- Parahaemophilia88776002
- Parahemophilia88776002
- Neonatal coagulation disorder95623001
- Hypoplasminogenaemia95840007
- Hypoplasminogenemia95840007
- Plasminogen deficiency95840007
- Hereditary hypoplasminogenaemia95841006
- Hereditary hypoplasminogenemia95841006
- Autosomal dominant deficiency of plasminogen95842004
- Autosomal dominant deficiency of profibrinolysin95842004
- Dysplasminogenaemia95844003
- Dysplasminogenemia95844003
- Hereditary dysfunctional plasminogen95845002
- Hereditary dysplasminogenaemia95845002
- Hereditary dysplasminogenemia95845002
- Dysfibrinogenaemia111589005
- Dysfibrinogenemia111589005
- Elevated fibrinogen level123791008
- Fibrinogen in blood above reference range123791008
- Platelet factor V deficiency (factor V Quebec)128101008
- Congenital afibrinogenaemia154818001
- Congenital afibrinogenemia154818001
- Contact factor deficiency234452003
- Passovoy factor deficiency234453008
- Prothrombin complex deficiency234454002
- Fibrinogen abnormality234455001
- Congenital fibrinogen abnormality234456000
- Hypodysfibrinogenaemia234458004
- Hypodysfibrinogenemia234458004
- Alpha chain defect dysfibrinogenaemia234459007
- Alpha chain defect dysfibrinogenemia234459007
- Beta chain defect dysfibrinogenaemia234460002
- Beta chain defect dysfibrinogenemia234460002
- Gamma chain defect dysfibrinogenaemia234461003
- Gamma chain defect dysfibrinogenemia234461003
- Fibrinolytic bleeding syndrome234464006
- Heparin cofactor II deficiency234468009
- Complement component 3 inactivator deficiency234621005
- Complement factor 3i deficiency234621005
- Factor I deficiency234621005
- Fibrinogen deficiency359727008
- Hereditary thrombophilic dysfibrinogenaemia438827002
- Hereditary thrombophilic dysfibrinogenemia438827002
- Hyperfibrinogenaemia439000005
- Hyperfibrinogenemia439000005
- Hereditary combined coagulation factor deficiency439157002
- Hereditary factor XIII A subunit deficiency439455002
- Hereditary factor XIII alpha subunit deficiency439455002
- Hereditary factor XIII type II deficiency439455002
- Factor I deficiency disease439458000
- Hereditary factor XIII B subunit deficiency439459008
- Hereditary factor XIII beta subunit deficiency439459008
- Hereditary factor XIII type III deficiency439459008
- Hereditary factor XIII A subunit and B subunit deficiency439460003
- Hereditary factor XIII type I deficiency439460003
- Combined deficiency of factor V and factor VIII715559004
- Factor V and factor VIII combined deficiency715559004
- Familial multiple coagulation factor deficiency715559004
- Congenital plasminogen activator inhibitor deficiency type 1717407006
- Hereditary combined deficiency of factors II, VII, IX and X724356003
- Hereditary combined deficiency of vitamin K-dependent clotting factors724356003
- Complete factor I deficiency783621008
- Immunodeficiency with factor I anomaly783621008
- Congenital Fletcher factor deficiency1162804003
- Hereditary congenital prekallikrein deficiency1162804003
- Factor V short isoforms related bleeding disorder1362024002
UMLS
- AC globulin deficiencyC0015499
- DEFIC FACTOR VC0015499
- Deficiencies, Factor 5C0015499
- Deficiencies, Factor FiveC0015499
- Deficiencies, Factor VC0015499
- Deficiencies, Labile FactorC0015499
- Deficiency, Factor 5C0015499
- Deficiency, Factor FiveC0015499
- Deficiency, Factor VC0015499
- Deficiency, Labile FactorC0015499
- Disease, OwrenC0015499
- Disease, Owren'sC0015499
- FACTOR V DEFICC0015499
- FACTOR V DEFICIENCYC0015499
- Factor 5 DeficienciesC0015499
- Factor 5 DeficiencyC0015499
- Factor Five DeficienciesC0015499
- Factor Five DeficiencyC0015499
- Factor V DeficienciesC0015499
- Factor V DeficiencyC0015499
- Hereditary Factor V DeficiencyC0015499
- Hereditary factor V deficiency diseaseC0015499
- Hereditary factor V deficiency disease (disorder)C0015499
- Hereditary hypoproaccelerinaemiaC0015499
- Hereditary hypoproaccelerinemiaC0015499
- LABILE FACTOR DEFICIENCYC0015499
- Labile Factor DeficienciesC0015499
- Labile Factor DeficiencyC0015499
- Labile factor deficiencyC0015499
- OWREN PARAHEMOPHILIAC0015499
- Owren DiseaseC0015499
- Owren ParahemophiliaC0015499
- Owren diseaseC0015499
- Owren's DiseaseC0015499
- Owren's diseaseC0015499
- Owrens DiseaseC0015499
- PARAHEMOPHILIAC0015499
- ParahaemophiliaC0015499
- ParahemophiliaC0015499
- Parahemophilia, OwrenC0015499
- ParahemophiliasC0015499
- Proaccelerin deficiencyC0015499
- deficiency factor vC0015499
- factor v deficienciesC0015499
- factor v deficiencyC0015499
- owren's diseaseC0015499
- parahemophiliaC0015499
- AFIBRINOGENEMIA, CONGENITALC2584774
- Afibrinogenaemia, CongenitalC2584774
- Afibrinogenaemias, CongenitalC2584774
- Afibrinogenemia, CongenitalC2584774
- Afibrinogenemia, FamilialC2584774
- Afibrinogenemias, CongenitalC2584774
- Afibrinogenemias, FamilialC2584774
- Congenital AfibrinogenaemiaC2584774
- Congenital AfibrinogenaemiasC2584774
- Congenital AfibrinogenemiaC2584774
- Congenital AfibrinogenemiasC2584774
- Congenital HypofibrinogenemiaC2584774
- Congenital HypofibrinogenemiasC2584774
- Congenital afibrinogenaemiaC2584774
- Congenital afibrinogenemiaC2584774
- Congenital afibrinogenemia (disorder)C2584774
- Congenital hypofibrinogenaemiaC2584774
- Congenital hypofibrinogenemiaC2584774
- Congenital hypofibrinogenemia (disorder)C2584774
- Familial AfibrinogenemiaC2584774
- Familial AfibrinogenemiasC2584774
- Familial afibrinogenemiaC2584774
- HYPOFIBRINOGENEMIA, CONGENITALC2584774
- Hypofibrinogenemia, CongenitalC2584774
- Hypofibrinogenemias, CongenitalC2584774
- Congenital dysfibrinogenaemiaC0272350
- Congenital dysfibrinogenemiaC0272350
- DYSFIBRINOGENEMIA, CONGENITALC0272350
- Dysfibrinogenemia (congenital)C0272350
- Dysfibrinogenemia, CongenitalC0272350
- Hereditary dysfibrinogenaemiaC0272350
- Hereditary dysfibrinogenemiaC0272350
- Hereditary dysfibrinogenemia (disorder)C0272350
- DEFIC FACTOR VIIC0015503
- Deficiencies, Factor 7C0015503
- Deficiencies, Factor SevenC0015503
- Deficiencies, Factor VIIC0015503
- Deficiency of stable factorC0015503
- Deficiency, Factor 7C0015503
- Deficiency, Factor SevenC0015503
- Deficiency, Factor VIIC0015503
- F7 - Factor VII deficiencyC0015503
- F7 DEFICIENCYC0015503
- F7 deficiencyC0015503
- FACTOR VII DEFICC0015503
- FACTOR VII DEFICIENCYC0015503
- Factor 7 DeficienciesC0015503
- Factor 7 DeficiencyC0015503
- Factor 7 deficiencyC0015503
- Factor Seven DeficienciesC0015503
- Factor Seven DeficiencyC0015503
- Factor VII DeficienciesC0015503
- Factor VII DeficiencyC0015503
- Factor VII deficiencyC0015503
- Factor VII deficiency (disorder)C0015503
- HYPOPROCONVERTINEMIAC0015503
- HypoproconvertinemiaC0015503
- HypoproconvertinemiasC0015503
- Proconvertin deficiencyC0015503
- Prothrombin conversion accelerator deficiencyC0015503
- Serum prothrombin conversion accelerator deficiencyC0015503
- Stable factor deficiencyC0015503
- disorder deficiency vii factorC0015503
- factor vii deficiencyC0015503
- DEFIC FIBRINOGENC4316812
- Deficiency factor IC4316812
- Deficiency of factor I [fibrinogen]C4316812
- Deficiency, FibrinogenC4316812
- FIBRINOGEN DEFICC4316812
- Factor I DeficiencyC4316812
- Factor I deficiencyC4316812
- Fibrinogen DeficienciesC4316812
- Fibrinogen DeficiencyC4316812
- Fibrinogen deficiencyC4316812
- Fibrinogen deficiency (disorder)C4316812
- HypofibrinogenemiaC4316812
- factor i deficiencyC4316812
- Deficiency of factor II [prothrombin]C3203356
- DysprothrombinemiaC3203356
- Factor II deficiencyC3203356
- Factor II deficiency (disorder)C3203356
- HypoprothrombinaemiaC3203356
- HypoprothrombinemiaC3203356
- Prothrombin deficiencyC3203356
- deficiency factor iiC3203356
- factor ii deficiencyC3203356
- hypoprothrombinaemiaC3203356
- hypoprothrombinemiaC3203356
- Deficiency of factor V [labile]C2873785
- Deficiency of factor VII [stable]C2873786
- Deficiency of factor X [Stuart-Prower]C2873787
- Deficiency of factor XII [Hageman]C2873788
- Deficiency of factor XIII [fibrin stabilizing]C2873789
- Hereditary deficiency of other clotting factorsC0494242
Frequently Asked Questions
What is ICD-10 code D68.2?
ICD-10-CM code D68.2 represents "Hereditary deficiency of other clotting factors". It is a billable/specific code that can be used on a claim.
Is D68.2 a billable code?
Yes, D68.2 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D68.2 in?
D68.2 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D68.2?
D68.2 has Excludes1 notes indicating codes that cannot be used together with it, including: abnormal coagulation profile NOS (R79.1).
What SNOMED CT codes does D68.2 map to?
D68.2 maps to 57 SNOMED CT concepts: 88776002, 64509006, 24149006, 234459007, 95842004, and 52 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D68.2?
D68.2 is linked to 12 UMLS Concept Unique Identifiers: C0015499, C2584774, C0272350, C0015503, C4316812, and 7 more. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.