D56.0
BillableAlpha thalassemia
Alpha thalassemia
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Alpha thalassemia major
- Hemoglobin H Constant Spring
- Hemoglobin H disease
- Hydrops fetalis due to alpha thalassemia
- Severe alpha thalassemia
- Triple gene defect alpha thalassemia
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Use Additional Code
Additional codes that should follow this code
- code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)
Also Known As / Clinical Terms
SNOMED CT
- Alpha thalassaemia major5300004
- Alpha thalassemia major5300004
- Haemoglobin Bart hydrops syndrome5300004
- Haemoglobin Bart's disease5300004
- Haemoglobin Bart's hydrops syndrome5300004
- Haemoglobin Barts hydrops5300004
- Hemoglobin Bart hydrops syndrome5300004
- Hemoglobin Bart's disease5300004
- Hemoglobin Bart's hydrops syndrome5300004
- Hemoglobin Barts hydrops5300004
- Alpha plus thalassaemia36467003
- Alpha plus thalassemia36467003
- Alpha thalassaemia 236467003
- Alpha thalassemia 236467003
- Haemoglobin S-F disease36472007
- Hemoglobin S-F disease36472007
- Microdrepanocytic disease36472007
- Microdrepanocytosis36472007
- Sickle cell thalassaemia disease36472007
- Sickle cell thalassemia disease36472007
- Sickle cell-thalassaemia disease36472007
- Sickle cell-thalassemia disease36472007
- Thalassaemia-haemoglobin S disease36472007
- Thalassemia-hemoglobin S disease36472007
- Haemoglobin H disease48553001
- Hemoglobin H disease48553001
- Alpha thalassaemia 166055002
- Alpha thalassemia 166055002
- Alpha zero thalassaemia66055002
- Alpha zero thalassemia66055002
- Alpha thalassaemia68913001
- Alpha thalassaemia syndrome68913001
- Alpha thalassemia68913001
- Alpha thalassemia syndrome68913001
- alpha thalassaemia68913001
- alpha thalassemia68913001
- Alpha plus thalassaemia non deletion type85422000
- Alpha plus thalassemia non deletion type85422000
- Alpha plus thalassaemia deletion type86242003
- Alpha plus thalassemia deletion type86242003
- Drepanocythaemia127040003
- Drepanocythemia127040003
- Haemoglobin S disease127040003
- Haemoglobin S-S disease127040003
- Hb S disease127040003
- Hb SS disease127040003
- Hemoglobin S disease127040003
- Hemoglobin S-S disease127040003
- Hereditary haemoglobinopathy disorder homozygous for haemoglobin S127040003
- Hereditary hemoglobinopathy disorder homozygous for hemoglobin S127040003
- Sickle cell anaemia127040003
- Sickle cell anemia127040003
- Sickle cell-haemoglobin SS disease127040003
- Sickle cell-hemoglobin SS disease127040003
- Sickle cell anaemia with coexistent alpha-thalassaemia127045008
- Sickle cell anemia with coexistent alpha-thalassemia127045008
- Fetal hereditary disease199531009
- Fetus with hereditary disease199531009
- Foetus with hereditary disease199531009
- Hereditary disorder of fetus199531009
- Homozygous alpha thalassaemia234383000
- Homozygous alpha thalassemia234383000
- HF - Hydrops fetalis276508000
- HF - Hydrops foetalis276508000
- Hydrops fetalis276508000
- Hydrops foetalis276508000
- Acquired haemoglobin H disease307343001
- Acquired hemoglobin H disease307343001
- Haemoglobin H constant spring thalassaemia447117006
- Hemoglobin H constant spring thalassemia447117006
- Fetal anaemia462166006
- Fetal anemia462166006
- Foetal anaemia462166006
- Alpha thalassaemia X-linked intellectual deficit715342005
- Alpha thalassaemia X-linked intellectual disability syndrome715342005
- Alpha thalassemia X-linked intellectual deficit715342005
- Alpha thalassemia X-linked intellectual disability syndrome715342005
- Deletion of part of short arm of chromosome 16726388008
- ATR-16 syndrome734349003
- Alpha thalassaemia intellectual disability syndrome, deletion type734349003
- Alpha thalassemia intellectual disability syndrome, deletion type734349003
- Alpha-thalassaemia intellectual disability syndrome linked to chromosome 16734349003
- Alpha-thalassemia intellectual disability syndrome linked to chromosome 16734349003
- Haemoglobin Paksé disease1148897000
- Hemoglobin Paksé disease1148897000
- Haemoglobin Seal Rock disease1148899002
- Hemoglobin Seal Rock disease1148899002
UMLS
- A-ThalassemiaC0002312
- ALPHA-THALASSEMIAC0002312
- Alpha ThalassemiaC0002312
- Alpha thalassaemiaC0002312
- Alpha thalassaemia syndromeC0002312
- Alpha thalassemiaC0002312
- Alpha thalassemia (disorder)C0002312
- Alpha thalassemia syndromeC0002312
- Alpha-thalassaemiaC0002312
- Alpha-thalassemiaC0002312
- Disease, Hemoglobin HC0002312
- HEMOGLOBIN H DISC0002312
- Hemoglobin H DiseaseC0002312
- Hemoglobin H diseaseC0002312
- Thalassaemia alphaC0002312
- Thalassemia alphaC0002312
- Thalassemia, AlphaC0002312
- Thalassemia-alphaC0002312
- alpha thalassaemiaC0002312
- alpha thalassemiaC0002312
- alpha thalassemiasC0002312
- alpha-ThalassemiaC0002312
- alpha-ThalassemiasC0002312
- alpha-thalassaemiaC0002312
- alpha-thalassemiaC0002312
- thalassemia alphaC0002312
- Î-thalassemiaC0002312
- Alpha thalassaemia majorC0272005
- Alpha thalassemia majorC0272005
- Haemoglobin Bart hydrops syndromeC0272005
- Haemoglobin Bart's diseaseC0272005
- Haemoglobin Bart's hydrops syndromeC0272005
- Haemoglobin Barts hydropsC0272005
- Hemoglobin Bart hydrops syndromeC0272005
- Hemoglobin Bart's diseaseC0272005
- Hemoglobin Bart's hydrops syndromeC0272005
- Hemoglobin Bart's hydrops syndrome (disorder)C0272005
- Hemoglobin Barts hydropsC0272005
- Haemoglobin H constant spring thalassaemiaC2960096
- Hemoglobin H Constant SpringC2960096
- Hemoglobin H constant spring thalassemiaC2960096
- Hemoglobin H constant spring thalassemia (disorder)C2960096
- Hydrops fetalis due to alpha thalassemiaC3161175
- Severe alpha thalassemiaC2873754
- Triple gene defect alpha thalassemiaC2873755
Frequently Asked Questions
What is ICD-10 code D56.0?
ICD-10-CM code D56.0 represents "Alpha thalassemia". It is a billable/specific code that can be used on a claim.
Is D56.0 a billable code?
Yes, D56.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D56.0 in?
D56.0 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D56.0?
D56.0 has Excludes1 notes indicating codes that cannot be used together with it, including: sickle-cell thalassemia (D57.4-); alpha thalassemia trait or minor (D56.3); asymptomatic alpha thalassemia (D56.3); and 2 more.
Are additional codes required with D56.0?
Yes, when using D56.0 you should also code: code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99).
What SNOMED CT codes does D56.0 map to?
D56.0 maps to 21 SNOMED CT concepts: 734349003, 307343001, 36467003, 86242003, 85422000, and 16 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D56.0?
D56.0 is linked to 6 UMLS Concept Unique Identifiers: C0002312, C0272005, C2960096, C3161175, C2873754, and 1 more. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.