4A01.00
Hereditary agammaglobulinaemia with profoundly reduced or absent B cells
Hereditary agammaglobulinaemia with profoundly reduced or absent B cells
Classification
ICD-11
Block
4A00-4A0ZParent Code
4A01.0ICD-10 Mapping
1 equivalentWHO Foundation
View on WHOICD-10 Equivalents(1)
ICD-10 Equivalents
View full mappingCorresponding ICD-10-CM codes from the WHO crosswalk mapping
Frequently Asked Questions
What is the ICD-11 code for hereditary agammaglobulinaemia with profoundly reduced or absent b cells?
The ICD-11 code for hereditary agammaglobulinaemia with profoundly reduced or absent b cells is 4A01.00. The full clinical description is "Hereditary agammaglobulinaemia with profoundly reduced or absent B cells".
What does ICD-11 code 4A01.00 mean?
ICD-11 code 4A01.00 represents “Hereditary agammaglobulinaemia with profoundly reduced or absent B cells”. It is classified under Chapter 4: Diseases of the Immune System.
What chapter is 4A01.00 in?
4A01.00 is in Chapter 4: Diseases of the Immune System (codes 4A00-4B4Z).
What is the ICD-10 equivalent of ICD-11 code 4A01.00?
4A01.00 maps to the ICD-10 code: D80.0 (Hereditary hypogammaglobulinemia). This is an equivalent mapping.
What is the difference between ICD-10 and ICD-11?
ICD-11 is the latest revision of the WHO's International Classification of Diseases, succeeding ICD-10. Key differences include: a fully digital-first design, new chapters for sleep-wake disorders, sexual health, and traditional medicine, improved coding for rare diseases, and better integration with electronic health records through extension codes.
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