Q04.1
BillableArhinencephaly
Arhinencephaly
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(8)
Q04.0Congenital malformations of corpus callosum
Q04.2Holoprosencephaly
Q04.3Other reduction deformities of brain
Q04.4Septo-optic dysplasia of brain
Q04.5Megalencephaly
Q04.6Congenital cerebral cysts
Q04.8Other specified congenital malformations of brain
Q04.9Congenital malformation of brain, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(30)
SNOMED CT
- Absent smell44169009
- Anosmia44169009
- Anosmia (loss of sense of smell)44169009
- Loss of sense of smell44169009
- Loss of the sense of smell44169009
- No sense of smell44169009
- Sense of smell absent44169009
- Sense of smell lost44169009
- Congenital anosmia230502003
- Disorder of smell275462005
- Isolated arhinencephaly771147003
UMLS
Clinical Terms
- Anosmia
- Loss of sense of smell
- Isolated arhinencephaly
- Congenital anosmia
- Anosmia (loss of sense of smell)
- Sense of smell absent
- Arhinencephalies
- arrhinencephaly
- Loss of the sense of smell
- Absent smell
- Sense of smell lost
- No sense of smell
- Disorder of smell
Frequently Asked Questions
What is the ICD-10 code for arhinencephaly?
The ICD-10-CM code for arhinencephaly is Q04.1. The full clinical description is "Arhinencephaly". Q04.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q04.1 mean?
ICD-10-CM code Q04.1 represents “Arhinencephaly”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q04.1 a billable code?
Yes, Q04.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q04.1 in?
Q04.1 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q04.1?
Q04.1 has Excludes1 notes indicating codes that cannot be used together with it, including: cyclopia (Q87.0); macrocephaly (Q75.3).
What SNOMED CT codes does Q04.1 map to?
Q04.1 maps to 4 SNOMED CT concepts: 44169009, 230502003, 275462005, 771147003. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q04.1?
Q04.1 is linked to 1 UMLS Concept Unique Identifier: C0078982. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q04.1 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like arhinencephaly affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q04.1?
Q04.1 maps to the ICD-11 code: LA05.4 (Arrhinencephaly).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.