M04.2

Billable

Cryopyrin-associated periodic syndromes

Cryopyrin-associated periodic syndromes

Status

Billable / Specific

Block

M04-M04

Parent Code

M04

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Chronic infantile neurological, cutaneous and articular syndrome [CINCA]
  • Familial cold autoinflammatory syndrome
  • Familial cold urticaria
  • Muckle-Wells syndrome
  • Neonatal onset multisystemic inflammatory disorder [NOMID]

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(3)
M04.1

Periodic fever syndromes

BillableM04.8

Other autoinflammatory syndromes

BillableM04.9

Autoinflammatory syndrome, unspecified

Billable
Also Known As / Clinical Terms(185)

SNOMED CT

UMLS

Clinical Terms

  • Familial Cold Induced Autoinflammatory Syndrome
  • Familial Cold Urticarias
  • Familial Cold Autoinflammatory Syndrome
  • Prieur-Griscelli Syndrome
  • Muckle-Wells syndrome
  • FCU - familial cold urticaria
  • Cold Induced Autoinflammatory Syndrome, Familial
  • Cold-induced angioedema-urticaria
  • FCAS
  • Syndrome, IOMID
  • Syndrome, UDA
  • Neonatal onset multisystem inflammatory disease
  • URTICARIA-DEAFNESS-AMYLOIDOSIS SYNDROME
  • COLD-INDUCED AUTOINFLAMMATORY SYNDROME, FAMILIAL
  • UDA Syndromes
  • Chronic infantile neurological, cutaneous and articular syndrome [CINCA]
  • IOMID Syndrome
  • CINCA - Chronic infantile neurological, cutaneous and articular syndrome
  • FCU
  • Neonatal onset multisystemic inflammatory disorder [NOMID]
  • CINCA/NOMID
  • IOMID
  • Cryopyrin-Associated Periodic Syndrome
  • IOMID Syndromes
  • Chronic Infantile Neurologic, Cutaneous, and Articular Syndrome
  • Cold urticaria
  • Chronic Neurologic Cutaneous and Articular Syndrome
  • CRYOPYRIN-ASSOCIATED PERIODIC SYNDROME 2
  • MWS
  • NOMID - Neonatal onset multisystem inflammatory disease
  • Familial Cold Urticaria
  • FACAS - F12-associated cold autoinflammatory syndrome
  • Amyloid nephropathy with deafness and urticaria
  • Cold Urticaria, Familial
  • Muckle-Wells type amyloidosis
  • Chronic infantile neurological, cutaneous and articular syndrome
  • CAPS3
  • Urticaria, Deafness and Amyloidosis
  • UDA SYNDROME
  • Cryopyrin Associated Periodic Syndrome
  • Familial cold urticaria (disorder)
  • Familial amyloid nephropathy with urticaria AND deafness (disorder)
  • Urticaria, Familial Cold
  • Cold-induced angio-oedema-urticaria
  • Chronic Neurologic, Cutaneous, and Articular Syndrome
  • Cryopyrin Associated Periodic Syndromes
  • Prieur-Griscelli Syndromes
  • Cryopyrin associated periodic syndrome (disorder)
  • Neonatal-onset multisystemic inflammatory disease
  • COLD HYPERSENSITIVITY
  • Prieur Griscelli Syndrome
  • Multisystem Inflammatory Disease, Neonatal-Onset
  • Infantile Onset Multisystem Inflammatory Disease
  • CRYOPYRIN-ASSOCIATED PERIODIC SYNDROME 3
  • Chronic Infantile Neurological, Cutaneous, and Articular Syndrome
  • Familial Cold-Induced Autoinflammatory Syndrome
  • CAPS2
  • CINCA Syndrome
  • Cryopyrinopathy
  • Multisystem Inflammatory Disease, Neonatal Onset
  • Chronic, Infantile, Neurological, Cutaneous, Articular Syndrome
  • Coagulation factor XII-associated cold autoinflammatory syndrome
  • Urticaria Deafness Amyloidosis Syndrome
  • Familial amyloid nephropathy with urticaria AND deafness
  • Muckle Wells Syndrome
  • Syndrome, Prieur-Griscelli
  • Urticaria-Deafness-Amyloidosis Syndromes
  • muckle well syndrome
  • CINCA
  • Chronic infantile neurological cutaneous and articular syndrome
  • Syndrome, Muckle-Wells
  • Chronic infantile neurological, cutaneous and articular syndrome (disorder)
  • Urticaria caused by cold
  • Neonatal-Onset Multisystem Inflammatory Disease
  • NOMID
  • FCAS - familial cold autoinflammatory syndrome
  • Cryopyrinopathies
  • Syndrome, Urticaria-Deafness-Amyloidosis
  • F12-associated cold autoinflammatory syndrome
Frequently Asked Questions
What is the ICD-10 code for cryopyrin-associated periodic syndromes?

The ICD-10-CM code for cryopyrin-associated periodic syndromes is M04.2. The full clinical description is "Cryopyrin-associated periodic syndromes". M04.2 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code M04.2 mean?

ICD-10-CM code M04.2 represents “Cryopyrin-associated periodic syndromes”. It is classified under Chapter 13: Diseases of the Musculoskeletal System and Connective Tissue and is a billable/specific code that can be used on a claim.

Is M04.2 a billable code?

Yes, M04.2 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is M04.2 in?

M04.2 is in Chapter 13: Diseases of the Musculoskeletal System and Connective Tissue (codes M00-M99).

What SNOMED CT codes does M04.2 map to?

M04.2 maps to 5 SNOMED CT concepts: 239826001, 1348303000, 74774004, 430079001, 238687000. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for M04.2?

M04.2 is linked to 5 UMLS Concept Unique Identifiers: C0268390, C0409818, C0343068, C2316212, C4268692. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does M04.2 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like cryopyrin-associated periodic syndromes affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of M04.2?

There is no direct ICD-11 mapping available for M04.2 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.