J84.89
BillableOther specified interstitial pulmonary diseases
Other specified interstitial pulmonary diseases
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Endogenous lipoid pneumonia
- Interstitial pneumonitis
- Non-specific interstitial pneumonitis NOS
- Organizing pneumonia NOS
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- •drug-induced interstitial lung disordersJ70.2-J70.4
- •interstitial emphysemaJ98.2
- •exogenous lipoid pneumoniaJ69.1
- •unspecified lipoid pneumoniaJ69.1
- •cryptogenic organizing pneumoniaJ84.116
- •idiopathic non-specific interstitial pneumonitisJ84.113
- •lipoid pneumonia, exogenous or unspecifiedJ69.1
- •lymphoid interstitial pneumoniaJ84.2
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •smoke inhalationT59.81
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •lung diseases due to external agentsJ60-J70
Code First
The underlying condition must be sequenced before this code
- , if applicable:
- •poisoning due to drug or toxin with fifth or sixth character to indicate intent), for toxic pneumonopathyT51-T65
- underlying cause of pneumonopathy, if known
Use Additional Code
Additional codes that should follow this code
- code, where applicable, to identify:
- •exposure to environmental tobacco smokeZ77.22
- •exposure to tobacco smoke in the perinatal periodP96.81
- •history of tobacco dependenceZ87.891
- •occupational exposure to environmental tobacco smokeZ57.31
- •tobacco dependenceF17
- •tobacco useZ72.0
- •code, for adverse effect, to identify drug with fifth or sixth character 5), if drug-inducedT36-T50
Code Also
A second code may be required; sequencing depends on circumstances
- , if applicable, associated condition
Related Codes(4)
Also Known As / Clinical Terms(127)
SNOMED CT
- Vineyard sprayers' hypersensitivity pneumonitis10785007
- Vineyard sprayers' lung10785007
- Vinyard sprayers' lung10785007
- Deficiency of DNA repair28965003
- Deficiency of deoxyribonucleic acid repair28965003
- Endogenous lipoid pneumonia42680007
- Endogenous lipoid pneumonitis42680007
- DNA repair65113001
- Deoxyribonucleic acid repair65113001
- Organised pneumonia68409003
- Organising pneumonitis68409003
- Organized pneumonia68409003
- Organizing pneumonitis68409003
- GIP - Giant cell interstitial pneumonitis192658007
- Giant cell interstitial pneumonitis192658007
- Cholesterol pneumonitis233728004
- UIP - Usual interstitial pneumonitis237121003
- Usual interstitial pneumonia237121003
- Usual interstitial pneumonitis237121003
- Chronic chemical respiratory disease266404004
- Lipid pneumonitis416916004
- Lipoid pneumonitis416916004
- CPI - chronic pneumonitis of infancy708026002
- Chronic pneumonitis of infancy708026002
- Acute endogenous lipoid pneumonia1010650005
- Acute endogenous lipoid pneumonitis1010650005
- Chronic endogenous lipoid pneumonia1010670004
- Chronic endogenous lipoid pneumonitis1010670004
- Interstitial lung disease due to ABCA3 (ATP-binding cassette subfamily A member 3) deficiency1222678003
- Interstitial lung disease due to ABCA3 deficiency1222678003
- Interstitial lung disease due to ATP-binding cassette subfamily A member 3 deficiency1222678003
- Interstitial pneumonitis1306604007
- Autosomal recessive deoxyribonucleic acid repair defect due to NSMCE3 deficiency1354861009
- Autosomal recessive deoxyribonucleic acid repair defect due to NSMCE3 mutation1354861009
- DNA repair defect due to NSMCE3 deficiency1354861009
- LICS syndrome1354861009
- Lung disease, immunodeficiency, chromosome breakage syndrome1354861009
- DPM - diffuse pulmonary meningotheliomatosis684633371000119107
- Diffuse pulmonary meningotheliomatosis684633371000119107
UMLS
- Endogenous Lipid PneumoniaC0264510
- Endogenous Lipid PneumoniasC0264510
- Endogenous Lipoid PneumoniaC0264510
- Endogenous Lipoid PneumoniasC0264510
- Endogenous lipoid pneumoniaC0264510
- Endogenous lipoid pneumonitisC0264510
- Endogenous lipoid pneumonitis (disorder)C0264510
- Lipid Pneumonia, EndogenousC0264510
- Lipoid Pneumonia, EndogenousC0264510
- Pneumonia, Endogenous LipidC0264510
- Pneumonia, Endogenous LipoidC0264510
- Interstitial PneumonitisC5887144
- Interstitial pneumonitisC5887144
- Interstitial pneumonitis (disorder)C5887144
- interstitial pneumonitisC5887144
- Non-specific interstitial pneumonitis NOSC3264402
- Organised pneumoniaC0264383
- Organising pneumoniaC0264383
- Organising pneumonitisC0264383
- Organized pneumoniaC0264383
- Organized pneumonia (disorder)C0264383
- Organizing PneumoniaC0264383
- Organizing PneumoniasC0264383
- Organizing pneumoniaC0264383
- Organizing pneumonia NOSC0264383
- Organizing pneumonitisC0264383
- Pneumonia, OrganizingC0264383
- organising pneumoniaC0264383
- organized pneumoniaC0264383
- organizing pneumoniaC0264383
- pneumonia organizingC0264383
- Other specified interstitial pulmonary diseasesC0348704
Clinical Terms
- DNA repair
- Lipid pneumonitis
- Chronic endogenous lipoid pneumonitis
- Endogenous lipoid pneumonitis (disorder)
- Pneumonia, Endogenous Lipoid
- Lipoid Pneumonia, Endogenous
- Pneumonia, Organizing
- GIP - Giant cell interstitial pneumonitis
- Organizing Pneumonias
- Interstitial pneumonitis
- Organizing Pneumonia
- Chronic endogenous lipoid pneumonia
- Acute endogenous lipoid pneumonitis
- Acute endogenous lipoid pneumonia
- CPI - chronic pneumonitis of infancy
- Usual interstitial pneumonitis
- Interstitial lung disease due to ATP-binding cassette subfamily A member 3 deficiency
- Giant cell interstitial pneumonitis
- Organizing pneumonia NOS
- Usual interstitial pneumonia
- Organising pneumonia
- Endogenous lipoid pneumonia
- Interstitial lung disease due to ABCA3 deficiency
- Deficiency of DNA repair
- Deoxyribonucleic acid repair
- Chronic pneumonitis of infancy
- Cholesterol pneumonitis
- Organized pneumonia
- Autosomal recessive deoxyribonucleic acid repair defect due to NSMCE3 deficiency
- Pneumonia, Endogenous Lipid
- Diffuse pulmonary meningotheliomatosis
- Endogenous Lipid Pneumonias
- LICS syndrome
- Lipoid pneumonitis
- Non-specific interstitial pneumonitis NOS
- Organized pneumonia (disorder)
- Organising pneumonitis
- Lipid Pneumonia, Endogenous
- Vineyard sprayers' lung
- Interstitial lung disease due to ABCA3 (ATP-binding cassette subfamily A member 3) deficiency
- Endogenous lipoid pneumonitis
- Autosomal recessive deoxyribonucleic acid repair defect due to NSMCE3 mutation
- Interstitial pneumonitis (disorder)
- Organised pneumonia
- UIP - Usual interstitial pneumonitis
- Endogenous Lipoid Pneumonias
- Vineyard sprayers' hypersensitivity pneumonitis
- Vinyard sprayers' lung
- Chronic chemical respiratory disease
- Endogenous Lipid Pneumonia
- Lung disease, immunodeficiency, chromosome breakage syndrome
- pneumonia organizing
- Organizing pneumonitis
- DNA repair defect due to NSMCE3 deficiency
- DPM - diffuse pulmonary meningotheliomatosis
- Deficiency of deoxyribonucleic acid repair
Frequently Asked Questions
What is the ICD-10 code for other specified interstitial pulmonary diseases?
The ICD-10-CM code for other specified interstitial pulmonary diseases is J84.89. The full clinical description is "Other specified interstitial pulmonary diseases". J84.89 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code J84.89 mean?
ICD-10-CM code J84.89 represents “Other specified interstitial pulmonary diseases”. It is classified under Chapter 10: Diseases of the Respiratory System and is a billable/specific code that can be used on a claim.
Is J84.89 a billable code?
Yes, J84.89 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is J84.89 in?
J84.89 is in Chapter 10: Diseases of the Respiratory System (codes J00-J99).
What codes cannot be used with J84.89?
J84.89 has Excludes1 notes indicating codes that cannot be used together with it, including: drug-induced interstitial lung disorders (J70.2-J70.4); interstitial emphysema (J98.2); exogenous lipoid pneumonia (J69.1); and 5 more.
Are additional codes required with J84.89?
Yes, when using J84.89, also report: code, where applicable, to identify:; exposure to environmental tobacco smoke (Z77.22); exposure to tobacco smoke in the perinatal period (P96.81); history of tobacco dependence (Z87.891); occupational exposure to environmental tobacco smoke (Z57.31); tobacco dependence (F17.-); tobacco use (Z72.0); code, for adverse effect, to identify drug (T36-T50 with fifth or sixth character 5), if drug-induced.
What SNOMED CT codes does J84.89 map to?
J84.89 maps to 17 SNOMED CT concepts: 1010650005, 1354861009, 708026002, 233728004, 266404004, and 12 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for J84.89?
J84.89 is linked to 5 UMLS Concept Unique Identifiers: C0264510, C5887144, C3264402, C0264383, C0348704. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does J84.89 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other specified interstitial pulmonary diseases affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of J84.89?
There is no direct ICD-11 mapping available for J84.89 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.