AutoICD API

94227-6

Laboratory

AGXT gene deletion+duplication and full mutation analysis in Blood or Tissue by Molecular genetics method

Definition

Full gene sequence analysis is performed to test for the presence of a mutation in all coding regions and intron/exon boundaries of the AGXT gene. Additionally, gene dosage analysis, such as by multiplex ligation-dependent probe amplification (MLPA), is used to test for the presence of large deletions and duplications in this gene. This test is useful for confirming a diagnosis of primary hyperoxaluria type 1 (PH1) and for testing at-risk individuals with a family history of PH1 in the absence of known mutations in the family.

LOINC 6-Axis Classification

Component

AGXT gene deletion+duplication & full mutation analysis

Property

Find

Time Aspect

Pt

System

Bld/Tiss

Scale Type

Doc

Method Type

Molgen

Details

Class

MOLPATH

Order/Observation

Both

Short Name

AGXT gene Del+Dup + Full Mut Anl Bld/T

Display Name

AGXT gene del+dup and full mutation analysis Molgen Doc (Bld/Tiss)

Related Names

2q37.3AGTAGT1AGXT1alanine-glyoxylate aminotransferaseAmplificationBloodDelDel+DupDel+Dup + Full Mut AnlDeletionsDocumentDpFindingFindingsfull gene sequencingFull Mut AnlGeneticsHeredityHeritableInheritedL-alanine: glyoxylate aminotransferase 1Molecular geneticsMolecular pathologyMOLPATHMutMutationsoxalosis IPCRPH1Point in timeprimary hyperoxaluria type 1Randomsequencing of entire coding regionserine:pyruvate aminotransferaseSPATSPTTissueTissue, unspecifiedTLH6WBWhole bloodWhole blood or Tissue

Frequently Asked Questions

What is LOINC code 94227-6?

LOINC code 94227-6 identifies "AGXT gene deletion+duplication and full mutation analysis in Blood or Tissue by Molecular genetics method". Full gene sequence analysis is performed to test for the presence of a mutation in all coding regions and intron/exon boundaries of the AGXT gene. Additionally, gene dosage analysis, such as by multiplex ligation-dependent probe amplification (MLPA), is used to test for the presence of large deletions and duplications in this gene. This test is useful for confirming a diagnosis of primary hyperoxaluria type 1 (PH1) and for testing at-risk individuals with a family history of PH1 in the absence of known mutations in the family.

What does 94227-6 measure?

This code measures AGXT gene deletion+duplication & full mutation analysis in Bld/Tiss. It belongs to the MOLPATH class in the LOINC classification.

What is LOINC?

LOINC (Logical Observation Identifiers Names and Codes) is a universal standard for identifying laboratory and clinical observations. It is maintained by the Regenstrief Institute and used worldwide for health data exchange.