AutoICD API

80154-8

Laboratory

Monolysocardiolipin/Cardiolipin [Molar ratio] in DBS

Definition

The ratio of monolysocardiolipin to cardiolipin in dried blood spots is measured as a diagnostic test for Barth syndrome (BTHS), an X-linked, metabolic, multi-system disorder characterized by cardiomyopathy, neutropenia, myopathy, and growth delay. [PMID: 18070816]

LOINC 6-Axis Classification

Component

Monolysocardiolipin/Cardiolipin

Property

SRto

Time Aspect

Pt

System

Bld.dot

Scale Type

Qn

Method Type

N/A

Details

Class

CHEM

Order/Observation

Both

Short Name

MLCL/CL DBS-sRto

Display Name

Monolysocardiolipin/Cardiolipin (DBS) [Molar ratio]

Related Names

BloodCardioCardiolipCardiolipnCardiolpnChemistryCLDBSDried blood spotFilter paperFPMLCLPoint in timeQNTQuanQuantQuantitativeRandomScrtoSubstance concentration ratioSubstance ratioWBWhole blood

Frequently Asked Questions

What is LOINC code 80154-8?

LOINC code 80154-8 identifies "Monolysocardiolipin/Cardiolipin [Molar ratio] in DBS". The ratio of monolysocardiolipin to cardiolipin in dried blood spots is measured as a diagnostic test for Barth syndrome (BTHS), an X-linked, metabolic, multi-system disorder characterized by cardiomyopathy, neutropenia, myopathy, and growth delay. [PMID: 18070816]

What does 80154-8 measure?

This code measures Monolysocardiolipin/Cardiolipin in Bld.dot. It belongs to the CHEM class in the LOINC classification.

What is LOINC?

LOINC (Logical Observation Identifiers Names and Codes) is a universal standard for identifying laboratory and clinical observations. It is maintained by the Regenstrief Institute and used worldwide for health data exchange.