Q85.89
BillableOther phakomatoses, not elsewhere classified
Other phakomatoses, not elsewhere classified
Status
Billable / Specific
Parent Code
Q85.8Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Peutz-Jeghers syndrome
- Sturge-Weber(-Dimitri) syndrome
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- inborn errors of metabolism (E70-E88)
Also Known As / Clinical Terms
SNOMED CT
- Centrofacial lentiginosis18822004
- Centrofacial lentiginosis syndrome18822004
- Angiomatosis oculo-orbital-thalamo-encephalic syndrome19886006
- Encephalocutaneous angiomatosis19886006
- Encephalofacial haemangiomatosis19886006
- Encephalofacial hemangiomatosis19886006
- Encephalotrigeminal angiomatosis19886006
- Neuroretinoangiomatosis19886006
- Sturge-Kalischer-Weber syndrome19886006
- Sturge-Weber disease19886006
- Sturge-Weber sequence19886006
- Sturge-Weber syndrome19886006
- Sturge-Weber-Dimitri syndrome19886006
- Peutz-Jeghers polyps of small bowel53633000
- PJS - Peutz-Jeghers syndrome54411001
- Perioral lentiginosis54411001
- Periorificial lentiginosis syndrome54411001
- Peutz-Jeghers polyposis54411001
- Peutz-Jeghers syndrome54411001
- Congenital leptomeningeal angiomatosis79801002
- Haemangioma of intracranial structure93468003
- Hemangioma of intracranial structure93468003
- Vascular neurocutaneous syndrome234139002
- Epidermal naevus syndrome239112008
- Epidermal nevus syndrome239112008
- Schimmelpeming Feuerstein Mims syndrome239112008
- Congenital arrector pili hamartoma239144007
- Congenital erector pili hamartoma239144007
- Congenital smooth muscle hamartoma239144007
- Naevus of pilar muscle239144007
- Nevus of pilar muscle239144007
- Smooth muscle naevus239144007
- Smooth muscle nevus239144007
- Diffuse smooth muscle hamartoma239145008
- Rhabdomyomatous mesenchymal hamartoma239146009
- Spinal hamartoma253125000
- Abnormality of canalisation and retrogressive differentiation253188000
- Abnormality of canalization and retrogressive differentiation253188000
- Hamartoma of intestine254594009
- Basal cell naevus with comedones254705003
- Basal cell nevus with comedones254705003
- Basaloid follicular hamartoma254705003
- Polyp of small intestine399723004
- Hamartoma of muscle399940000
- Hamartoma of pilosebaceous apparatus400120004
- Port-wine stain with associated anomalies403544009
- Phakomatosis pigmentovascularis403545005
- Port-wine stain with oculocutaneous melanosis403545005
- Hereditary neurocutaneous angiomata403775003
- Hereditary neurocutaneous vascular malformations403775003
- Hereditary cutaneous vascular syndrome403776002
- Angiomatosis of meninges445135003
- Phakomatosis cesioflammea703284009
- Phakomatosis spilorosea703285005
- Phakomatosis caesiomarmorata703286006
- Phakomatosis cesiomarmorata703286006
- Naevus sebaceous707136009
- Naevus sebaceous of Jadassohn707136009
- Nevus sebaceous707136009
- Nevus sebaceous of Jadassohn707136009
- Organoid naevus707136009
- Organoid nevus707136009
- Sebaceous naevus707136009
- Sebaceous nevus707136009
- Hamartoma of small intestine721665000
- Perlman syndrome722231005
- Phakomatosis pigmentokeratotica723455009
- Generalised basaloid follicular hamartoma syndrome766928004
- Generalized basaloid follicular hamartoma syndrome766928004
- SCALP syndrome774208009
- Sebaceous naevus, central nervous system malformations, aplasia cutis congenita, limbal dermoid, pigmented naevus syndrome774208009
- Sebaceous nevus, central nervous system malformations, aplasia cutis congenita, limbal dermoid, pigmented nevus syndrome774208009
- Congenital rhabdomyomatous mesenchymal hamartoma787472005
- Gingival enlargement due to Sturge-Weber syndrome1172358003
UMLS
- Angiomatosis Oculoorbital-Thalamic SyndromeC0038505
- Angiomatosis aculoorbital-thalamic syndromeC0038505
- Angiomatosis oculo-orbital-thalamo-encephalic syndromeC0038505
- Angiomatosis, Meningo-Oculo-FacialC0038505
- Encephalocutaneous angiomatosisC0038505
- Encephalofacial Hemangiomatosis SyndromeC0038505
- Encephalofacial haemangiomatosisC0038505
- Encephalofacial hemangiomatosisC0038505
- Encephalofacial hemangiomatosis syndromeC0038505
- Encephalotrigeminal SyndromeC0038505
- Encephalotrigeminal angiomatosisC0038505
- Hemangiomatosis Syndrome, EncephalofacialC0038505
- Meningo Oculo Facial AngiomatosisC0038505
- Meningo-Oculo-Facial AngiomatosisC0038505
- Meningo-oculo-facial angiomatosisC0038505
- Meningofacial Angiomatosis-Cerebral Calcification SyndromeC0038505
- Meningofacial angiomatosis-cerebral calcification syndromeC0038505
- Milles' syndromeC0038505
- NeuroretinoangiomatosisC0038505
- Phakomatosis, Sturge WeberC0038505
- Phakomatosis, Sturge-WeberC0038505
- STURGE DISC0038505
- STURGE-WEBER SYNDROMEC0038505
- SWSC0038505
- Schirmer's syndromeC0038505
- Sturge DiseaseC0038505
- Sturge Kalischer Weber SyndromeC0038505
- Sturge SyndromeC0038505
- Sturge Weber Dimitri SyndromeC0038505
- Sturge Weber Krabbe SyndromeC0038505
- Sturge Weber SyndromeC0038505
- Sturge's SyndromeC0038505
- Sturge-Kalischer-Weber SyndromeC0038505
- Sturge-Kalischer-Weber syndromeC0038505
- Sturge-Weber DiseaseC0038505
- Sturge-Weber PhakomatosisC0038505
- Sturge-Weber SyndromeC0038505
- Sturge-Weber diseaseC0038505
- Sturge-Weber sequenceC0038505
- Sturge-Weber syndromeC0038505
- Sturge-Weber syndrome (disorder)C0038505
- Sturge-Weber(-Dimitri) syndromeC0038505
- Sturge-Weber-Dimitri SyndromeC0038505
- Sturge-Weber-Dimitri syndromeC0038505
- Sturge-Weber-Krabbe SyndromeC0038505
- Sturge-Weber-Krabbe syndromeC0038505
- Syndrome, Encephalofacial HemangiomatosisC0038505
- Syndrome, SturgeC0038505
- Syndrome, Sturge'sC0038505
- Syndrome, Sturge-Kalischer-WeberC0038505
- Syndrome, Sturge-WeberC0038505
- Syndrome, Sturge-Weber-DimitriC0038505
- Syndrome, Sturge-Weber-KrabbeC0038505
- neurocutaneous syndromeC0038505
- sturge syndrome weberC0038505
- sturge weber diseaseC0038505
- sturge weber syndromeC0038505
- sturge-weber diseaseC0038505
- sturge-weber syndromeC0038505
- sturges syndrome weberC0038505
- sturges weber syndromeC0038505
- syndrome webersC0038505
- weber syndromeC0038505
- webers syndromeC0038505
- Hamartomatous Intestinal PolyposesC0031269
- Hamartomatous Intestinal PolyposisC0031269
- Intestinal Polyposes, HamartomatousC0031269
- Intestinal Polyposis, HamartomatousC0031269
- Intestinal polyposis-cutaneous pigmentation syndromeC0031269
- Jeghers-Peutz SyndromeC0031269
- Lentiginoses, PerioralC0031269
- Lentiginosis, PerioralC0031269
- Lentiginosis, perioralC0031269
- PEUTZ-JEGHERS SYNDROMEC0031269
- PJSC0031269
- PJS - Peutz-Jeghers syndromeC0031269
- POLYPOSIS, HAMARTOMATOUS INTESTINALC0031269
- POLYPS-AND-SPOTS SYNDROMEC0031269
- Perioral LentiginosesC0031269
- Perioral LentiginosisC0031269
- Perioral lentiginosisC0031269
- Periorificial Lentiginosis SyndromeC0031269
- Periorificial Lentiginosis SyndromesC0031269
- Periorificial lentiginosis syndromeC0031269
- Peutz Jegher's SyndromeC0031269
- Peutz Jeghers PolyposisC0031269
- Peutz Jeghers SyndromeC0031269
- Peutz Jeghers syndromeC0031269
- Peutz's SyndromeC0031269
- Peutz-Jegher SyndromeC0031269
- Peutz-Jegher's SyndromeC0031269
- Peutz-Jeghers PolyposisC0031269
- Peutz-Jeghers SyndromeC0031269
- Peutz-Jeghers polyposisC0031269
- Peutz-Jeghers syndromeC0031269
- Peutz-Jeghers syndrome (disorder)C0031269
- Polyposes, Hamartomatous IntestinalC0031269
- Polyposis, Hamartomatous IntestinalC0031269
- Polyposis, Peutz-JeghersC0031269
- Polyposis, hamartomatous intestinalC0031269
- Polyposis, intestinal, IIC0031269
- Polyps and Spots SyndromeC0031269
- Polyps-and-Spots SyndromeC0031269
- Polyps-and-Spots SyndromesC0031269
- Polyps-and-spots syndromeC0031269
- Syndrome, Periorificial LentiginosisC0031269
- Syndrome, Peutz-Jegher'sC0031269
- Syndrome, Peutz-JeghersC0031269
- Syndrome, Polyps-and-SpotsC0031269
- Syndromes, Periorificial LentiginosisC0031269
- Syndromes, Polyps-and-SpotsC0031269
- peutz jegher syndromeC0031269
- peutz jeghers syndromeC0031269
- peutz jeghers syndromesC0031269
- peutz-jegher syndromeC0031269
- peutz-jegher's syndromeC0031269
- peutz-jeghers syndromeC0031269
- syndrome peutz-jeghersC0031269
- Other phakomatoses, not elsewhere classifiedC0869082
Frequently Asked Questions
What is ICD-10 code Q85.89?
ICD-10-CM code Q85.89 represents "Other phakomatoses, not elsewhere classified". It is a billable/specific code that can be used on a claim.
Is Q85.89 a billable code?
Yes, Q85.89 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q85.89 in?
Q85.89 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q85.89?
Q85.89 has Excludes1 notes indicating codes that cannot be used together with it, including: ataxia telangiectasia [Louis-Bar] (G11.3); familial dysautonomia [Riley-Day] (G90.1); Meckel-Gruber syndrome (Q61.9).
What SNOMED CT codes does Q85.89 map to?
Q85.89 maps to 34 SNOMED CT concepts: 253188000, 19886006, 445135003, 254705003, 18822004, and 29 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q85.89?
Q85.89 is linked to 3 UMLS Concept Unique Identifiers: C0038505, C0031269, C0869082. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.