E88.9
BillableMetabolic disorder, unspecified
Metabolic disorder, unspecified
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
- histiocytosis X (chronic) (C96.6)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Use Additional Code
Additional codes that should follow this code
- codes for associated conditions
Also Known As / Clinical Terms
SNOMED CT
- Disorder of neurometabolic regulation16279005
- Metabolic myopathy26111005
- Myopathy in metabolic diseases26111005
- Generalised metabolic disorder30390004
- Generalized metabolic disorder30390004
- Restrictive cardiomyopathy secondary to familial storage disease30884007
- Storage disease34420000
- Familial cardiomyopathy35728003
- Primary familial cardiomyopathy35728003
- Arthropathy associated with an endocrine AND/OR metabolic disorder39710007
- Arthropathy associated with endocrine and metabolic disorder39710007
- Corneal deposit associated with metabolic disorder43521007
- Nutritional myopathy44253006
- Age-related hearing loss49526009
- Presbyacusia49526009
- Presbycusis49526009
- Senile deafness49526009
- Sinus bradycardia49710005
- Metabolic bone disease50279003
- Metabolic disorder of bone50279003
- Metabolic disturbance in labor AND/OR delivery61714007
- Metabolic disturbance in labour AND/OR delivery61714007
- Defective metabolism63569001
- BIH - Benign intracranial hypertension68267002
- Benign intracranial hypertension68267002
- IIH - Idiopathic intracranial hypertension68267002
- Idiopathic intracranial hypertension68267002
- Noninfective serous meningitis68267002
- Nonne's syndrome68267002
- Otitic hydrocephalus syndrome68267002
- Pseudotumor cerebri68267002
- Pseudotumour cerebri68267002
- Localised metabolic disorder74479008
- Localized metabolic disorder74479008
- MD - Metabolic disorders75934005
- Metabolic disease75934005
- Metabolic disorder75934005
- Enzyme disorder78548001
- Enzymopathy78548001
- Amino acid deficiency82994006
- IBEM - Inborn error of metabolism86095007
- IEM - Inborn error of metabolism86095007
- Inborn error of metabolism86095007
- Abnormal metabolic requirement87133009
- Defective biosynthesis102632006
- Metabolic disorders of the kidney106000008
- Metabolic renal disease106000008
- Dilated cardiomyopathy due to metabolic disorder111285003
- Dilated cardiomyopathy secondary to metabolic disorder111285003
- Metabolic cardiomyopathy111285003
- Acute metabolic disease127339009
- Acute metabolic disorder127339009
- Inherited metabolic disorder of nervous system128190004
- Chronic metabolic disease128289001
- Chronic metabolic disorder128289001
- Metabolic presbycusis129629004
- Acute confusional state, of metabolic origin191504009
- Glaucoma in endocrine, nutritional and metabolic diseases193556009
- Cardiac glycogenosis195025008
- Cardiomyopathy due to mucopolysaccharidosis195027000
- Mucopolysaccharidosis cardiomyopathy195027000
- Familial restrictive cardiomyopathy233878008
- Intrinsic staining of tooth - metabolic disease234985000
- Metabolic ileus235836004
- Metabolic and genetic disorder affecting the liver235903001
- Abnormal metabolic state due to diabetes mellitus237620003
- Abnormal metabolic state in diabetes mellitus237620003
- Metabolic and nutritional disorders affecting skin238944001
- Metabolic complication of procedures363203000
- Seizures due to metabolic disorder371022006
- Clinical manifestation of enzyme deficiency410053003
- Aplastic anaemia associated with metabolic alteration413565006
- Aplastic anemia associated with metabolic alteration413565006
- Thrombocytopenic purpura associated with metabolic disorder417626001
- Carnitine deficiency421784001
- Acquired sensorineural hearing loss609125008
- Pericarditis due to metabolic disease703332001
- Pericarditis in metabolic disease703332001
- Neuropathy of upper limb due to metabolic disorder710349003
- Peripheral neuropathy of upper limb due to metabolic disorder710349003
- Peripheral neuropathy due to metabolic disorder710360007
- Tremor due to metabolic disorder722969006
- Dementia due to metabolic abnormality722979008
- Myelopathy due to metabolic disorder722984002
- Neonatal metabolic disorder736652002
- Interstitial lung disease due to metabolic disease737183007
- Anaemia due to metabolic disorder737220002
- Anemia due to metabolic disorder737220002
- Metabolic anaemia737220002
- Metabolic anemia737220002
- Autonomic neuropathy due to metabolic disease737241008
- Navajo neurohepatopathy784346006
- Navajo neuropathy784346006
- Radiculopathy due to metabolic disorder789018001
- Cardiomyopathy due to storage disease860839005
- Infiltrative cardiomyopathy871646007
- Sinus bradycardia due to metabolic disease1142111009
- Chronic tubulointerstitial nephritis due to metabolic disease1144897006
- Disorder of nerve due to metabolic disease1153623003
- Metabolic neuropathy1153623003
- Enlargement of spleen due to storage disease1162654006
- Splenomegaly due to storage disease1162654006
- Hypopituitarism due to metabolic disease1186837006
- Corneal deposits due to metabolic disorder1217638003
- Autonomic disorder due to metabolic disorder1259056005
- Disorder of autonomic nervous system due to metabolic disorder1259056005
- Metabolic autonomic disorder1259056005
- Chorea due to metabolic disorder1259619002
- Chorea due to inborn error of metabolism1259622000
- Benign intracranial hypertension due to metabolic disease1263545007
- Arthropathy due to metabolic disorder324301000119107
- Bilateral deposit in corneas678881000119107
- Corneal deposit in bilateral eyes678881000119107
- Deposit in bilateral corneas678881000119107
- Deposit in both corneas678881000119107
- Carnitine deficiency due to inborn error of metabolism55341000119107
- Corneal deposit of bilateral eyes due to metabolic disorder678941000119106
- Deposit in cornea of bilateral eyes due to metabolic disorder678941000119106
- Deposit in cornea of both eyes due to metabolic disorder678941000119106
- Corneal deposit of left eye due to metabolic disorder678951000119108
- Deposit in cornea of left eye due to metabolic disorder678951000119108
- Corneal deposit of right eye due to metabolic disorder680981000119105
- Deposit in cornea of right eye due to metabolic disorder680981000119105
- Hereditary metabolic disease1821000146108
UMLS
- DIS METABC0025517
- Disease, MetabolicC0025517
- Diseases, MetabolicC0025517
- Generalised metabolic disorderC0025517
- Generalized metabolic disorderC0025517
- Generalized metabolic disorder (disorder)C0025517
- MD - Metabolic disordersC0025517
- METAB DISC0025517
- Metabolic DiseaseC0025517
- Metabolic DiseasesC0025517
- Metabolic DisorderC0025517
- Metabolic DisordersC0025517
- Metabolic diseaseC0025517
- Metabolic disease (disorder)C0025517
- Metabolic disorderC0025517
- Metabolic disorder NOSC0025517
- Metabolic disorder, unspecifiedC0025517
- ThesaurismosesC0025517
- ThesaurismosisC0025517
- Unspecified disorder of metabolismC0025517
- metabolic diseaseC0025517
- metabolic diseasesC0025517
- metabolic disorderC0025517
- metabolic disordersC0025517
- metabolism disorderC0025517
Frequently Asked Questions
What is ICD-10 code E88.9?
ICD-10-CM code E88.9 represents "Metabolic disorder, unspecified". It is a billable/specific code that can be used on a claim.
Is E88.9 a billable code?
Yes, E88.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E88.9 in?
E88.9 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E88.9?
E88.9 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 4 more.
Are additional codes required with E88.9?
Yes, when using E88.9 you should also code: codes for associated conditions.
What SNOMED CT codes does E88.9 map to?
E88.9 maps to 76 SNOMED CT concepts: 87133009, 237620003, 609125008, 191504009, 127339009, and 71 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E88.9?
E88.9 is linked to 1 UMLS Concept Unique Identifier: C0025517. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.