E83.110
BillableHereditary hemochromatosis
Hereditary hemochromatosis
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Bronzed diabetes
- Pigmentary cirrhosis (of liver)
- Primary (hereditary) hemochromatosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
- dietary mineral deficiency (E58-E61)
- parathyroid disorders (E20-E21)
- vitamin D deficiency (E55.-)
- iron deficiency anemia (D50.-)
- sideroblastic anemia (D64.0-D64.3)
- GALD (P78.84)
- Gestational alloimmune liver disease (P78.84)
- Neonatal hemochromatosis (P78.84)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Also Known As / Clinical Terms
SNOMED CT
- Familial haemochromatosis35400008
- Familial hemochromatosis35400008
- Hereditary haemochromatosis35400008
- Hereditary hemochromatosis35400008
- Hypochromic microcytic anaemia44666001
- Hypochromic microcytic anemia44666001
- Microcytic hypochromic anaemia44666001
- Microcytic hypochromic anemia44666001
- HJV or HAMP-related haemochromatosis50855007
- HJV or HAMP-related hemochromatosis50855007
- Haemochromatosis type 250855007
- Hemochromatosis type 250855007
- Juvenile haemochromatosis50855007
- Juvenile hemochromatosis50855007
- Bronze cirrhosis78208005
- Pigment cirrhosis78208005
- Pigmentary cirrhosis of liver78208005
- Bronze diabetes399144008
- Bronzed diabetes399144008
- Primary haemochromatosis399170009
- Primary hemochromatosis399170009
- Hypochromic microcytic anaemia with iron overload711161006
- Hypochromic microcytic anemia with iron overload711161006
- Microcytic anaemia and hepatic iron overload711161006
- Microcytic anaemia with liver iron overload711161006
- Microcytic anemia and hepatic iron overload711161006
- Microcytic anemia with liver iron overload711161006
- Haemochromatosis type 3719974003
- Hemochromatosis type 3719974003
- TFR2 (transferrin receptor 2 gene) related haemochromatosis719974003
- TFR2 (transferrin receptor 2 gene) related hemochromatosis719974003
- Autosomal dominant hereditary haemochromatosis719975002
- Autosomal dominant hereditary hemochromatosis719975002
- Haemochromatosis due to defect in ferroportin719975002
- Haemochromatosis type 4719975002
- Hemochromatosis due to defect in ferroportin719975002
- Hemochromatosis type 4719975002
- Type 2B juvenile hereditary haemochromatosis1186844002
- Type 2B juvenile hereditary hemochromatosis1186844002
- HFE related haemochromatosis1186847009
- HFE related hemochromatosis1186847009
- Haemochromatosis type 11186847009
- Hemochromatosis type 11186847009
- Type 2A juvenile hereditary haemochromatosis1186849007
- Type 2A juvenile hereditary hemochromatosis1186849007
- FTH1 (ferritin heavy chain 1) related iron overload1230310007
- FTH1-associated iron overload1230310007
- FTH1-related iron overload1230310007
- Ferritin heavy chain 1-related iron overload1230310007
- Symptomatic form of classic haemochromatosis1237181009
- Symptomatic form of classic hemochromatosis1237181009
- Symptomatic form of haemochromatosis type 11237181009
- Symptomatic form of hemochromatosis type 11237181009
- Digenic haemochromatosis1299153008
- Digenic hemochromatosis1299153008
- SLC40A1-related haemochromatosis1303910000
- SLC40A1-related hemochromatosis1303910000
- Solute carrier family 40 member 1-related haemochromatosis1303910000
- Solute carrier family 40 member 1-related hemochromatosis1303910000
- Ferroportin disease1303911001
- Haemochromatosis type 4A1303911001
- Hemochromatosis type 4A1303911001
UMLS
- Bronze DiabetesC0018995
- Bronze diabetesC0018995
- Bronze diabetes (disorder)C0018995
- Bronzed CirrhosesC0018995
- Bronzed CirrhosisC0018995
- Bronzed diabetesC0018995
- Cirrhoses, BronzedC0018995
- Cirrhoses, PigmentaryC0018995
- Cirrhosis, BronzedC0018995
- Cirrhosis, PigmentaryC0018995
- Diabetes, BronzeC0018995
- Disease, Von Recklenhausen-ApplebaumC0018995
- Diseases, Von Recklenhausen-ApplebaumC0018995
- Disorder, Iron StorageC0018995
- Disorders, Iron StorageC0018995
- HaemochromatosesC0018995
- HaemochromatosisC0018995
- HemochromatoseC0018995
- HemochromatosesC0018995
- HemochromatosisC0018995
- Hemochromatosis (disorder)C0018995
- Hemochromatosis, unspecifiedC0018995
- HemosiderosisC0018995
- Iron Overload DiseaseC0018995
- Iron Storage DisorderC0018995
- Iron Storage DisordersC0018995
- Iron overload diseaseC0018995
- Iron storage diseaseC0018995
- Iron storage disorderC0018995
- Pigmentary CirrhosesC0018995
- Pigmentary CirrhosisC0018995
- Recklenhausen-Applebaum Disease, VonC0018995
- Recklenhausen-Applebaum Diseases, VonC0018995
- Storage Disorder, IronC0018995
- Storage Disorders, IronC0018995
- Syndrome, Troisier-Hanot-ChauffardC0018995
- Syndromes, Troisier-Hanot-ChauffardC0018995
- Troisier Hanot Chauffard SyndromeC0018995
- Troisier-Hanot-Chauffard SyndromeC0018995
- Troisier-Hanot-Chauffard SyndromesC0018995
- Troisier-Hanot-Chauffard syndromeC0018995
- Von Recklenhausen Applebaum DiseaseC0018995
- Von Recklenhausen-Applebaum DiseaseC0018995
- Von Recklenhausen-Applebaum DiseasesC0018995
- Von Recklenhausen-Applebaum diseaseC0018995
- bronze diabetesC0018995
- bronzed diabetesC0018995
- diabetes bronzeC0018995
- disorders iron storageC0018995
- haemochromatosisC0018995
- hemochromatosesC0018995
- hemochromatosisC0018995
- iron storage diseaseC0018995
- iron storage disorderC0018995
- Bronze cirrhosisC1442995
- Bronzed cirrhosisC1442995
- Pigment cirrhosisC1442995
- Pigment cirrhosis (disorder)C1442995
- Pigmentary cirrhosisC1442995
- Pigmentary cirrhosis (of liver)C1442995
- Pigmentary cirrhosis of liverC1442995
- Familial HemochromatosesC0392514
- Familial HemochromatosisC0392514
- Familial haemochromatosisC0392514
- Familial hemochromatosisC0392514
- Genetic HemochromatosesC0392514
- Genetic HemochromatosisC0392514
- Genetic hemochromatosisC0392514
- HEMOCHROMATOSIS, HEREDITARYC0392514
- HLAHC0392514
- Hemochromatoses, FamilialC0392514
- Hemochromatoses, GeneticC0392514
- Hemochromatosis, FamilialC0392514
- Hemochromatosis, GeneticC0392514
- Hereditary HemochromatosisC0392514
- Hereditary haemochromatosisC0392514
- Hereditary hemochromatosisC0392514
- Hereditary hemochromatosis (disorder)C0392514
- Idiopathic haemochromatosisC0392514
- Idiopathic hemochromatosisC0392514
- Idiopathic hemochromatosis (disorder)C0392514
- Primary HemochromatosisC0392514
- Primary haemochromatosisC0392514
- Primary hemochromatosisC0392514
- Primary hemochromatosis (disorder)C0392514
- familial haemochromatosisC0392514
- familial hemochromatosisC0392514
- hemochromatosis hereditaryC0392514
- hereditary haemochromatosisC0392514
- hereditary hemochromatosisC0392514
- idiopathic hemochromatosisC0392514
- primary haemochromatosisC0392514
- primary hemochromatosisC0392514
- Primary (hereditary) hemochromatosisC2921013
Frequently Asked Questions
What is the ICD-10 code for hereditary hemochromatosis?
The ICD-10-CM code for hereditary hemochromatosis is E83.110. The full clinical description is "Hereditary hemochromatosis". E83.110 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E83.110 mean?
ICD-10-CM code E83.110 represents "Hereditary hemochromatosis". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E83.110 a billable code?
Yes, E83.110 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E83.110 in?
E83.110 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E83.110?
E83.110 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 11 more.
What SNOMED CT codes does E83.110 map to?
E83.110 maps to 17 SNOMED CT concepts: 719975002, 78208005, 399144008, 1299153008, 1230310007, and 12 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E83.110?
E83.110 is linked to 4 UMLS Concept Unique Identifiers: C0018995, C1442995, C0392514, C2921013. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.