E78.1
BillablePure hyperglyceridemia
Pure hyperglyceridemia
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Elevated fasting triglycerides
- Endogenous hyperglyceridemia
- Fredrickson's hyperlipoproteinemia, type IV
- Hyperlipidemia, group B
- Hyperprebetalipoproteinemia
- Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinemia
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
- sphingolipidosis (E75.0-E75.3)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Also Known As / Clinical Terms
SNOMED CT
- Hyperlipoproteinaemia3744001
- Hyperlipoproteinemia3744001
- Familial hypertriglyceridaemia34528009
- Familial hypertriglyceridemia34528009
- Endogenous hyperlipaemia129589009
- Endogenous hyperlipemia129589009
- Endogenous hyperlipidaemia129589009
- Endogenous hyperlipidemia129589009
- Primary hypertriglyceridaemia238083002
- Primary hypertriglyceridemia238083002
- Very low density lipoprotinaemia238084008
- Very low density lipoprotinemia238084008
- Fredrickson type IV hyperlipoproteinaemia238085009
- Fredrickson type IV hyperlipoproteinemia238085009
- Fredrickson type IV lipidaemia238085009
- Fredrickson type IV lipidemia238085009
- Secondary hypertriglyceridaemia238087001
- Secondary hypertriglyceridemia238087001
- Pure hyperglyceridaemia267433009
- Pure hyperglyceridemia267433009
- Hypertriglyceridaemia302870006
- Hypertriglyceridemia302870006
- Sporadic primary hypertriglyceridaemia402473001
- Sporadic primary hypertriglyceridemia402473001
- Xanthoma due to abnormality of lipid metabolism402724009
- Primary genetic hyperlipidaemia402785008
- Primary genetic hyperlipidemia402785008
- Transient infantile hypertriglyceridaemia and fatty liver773649005
- Transient infantile hypertriglyceridaemia and hepatosteatosis773649005
- Transient infantile hypertriglyceridemia and fatty liver773649005
- Transient infantile hypertriglyceridemia and hepatosteatosis773649005
- Xanthoma due to primary hypertriglyceridaemia1256071008
- Xanthoma due to primary hypertriglyceridemia1256071008
UMLS
- CARBOHYDRATE-INDUCIBLE HYPERLIPEMIAC0020480
- Carbohydrate Inducible HyperlipemiaC0020480
- Carbohydrate Inducible HyperlipemiasC0020480
- Carbohydrate-Inducible HyperlipemiaC0020480
- Carbohydrate-Inducible HyperlipemiasC0020480
- Endogenous hyperglyceridemiaC0020480
- Endogenous hyperlipaemiaC0020480
- Endogenous hyperlipemiaC0020480
- Endogenous hyperlipidaemiaC0020480
- Endogenous hyperlipidemiaC0020480
- Endogenous hyperlipidemia (disorder)C0020480
- Familial Hyperlipoproteinemia Type 4C0020480
- Familial HypertriglyceridemiaC0020480
- Familial Type IV HyperlipoproteinemiaC0020480
- Familial hypertriglyceridaemiaC0020480
- Familial hypertriglyceridemiaC0020480
- Familial hypertriglyceridemia (disorder)C0020480
- Fredrickson Type IV LipidemiaC0020480
- Fredrickson Type IV lipidaemiaC0020480
- Fredrickson Type IV lipidemiaC0020480
- Fredrickson type IV hyperlipoproteinaemiaC0020480
- Fredrickson type IV hyperlipoproteinemiaC0020480
- Fredrickson type IV hyperlipoproteinemia (disorder)C0020480
- Fredrickson type IV lipidaemiaC0020480
- Fredrickson type IV lipidemiaC0020480
- Fredrickson's hyperlipoproteinemia, type IVC0020480
- HYPERLIPOPROTEINEMIA, TYPE IVC0020480
- Hyper prebeta lipoproteinemiaC0020480
- Hyperlipemia, Carbohydrate InducibleC0020480
- Hyperlipemia, Carbohydrate-InducibleC0020480
- Hyperlipemias, Carbohydrate InducibleC0020480
- Hyperlipemias, Carbohydrate-InducibleC0020480
- Hyperlipidemia, group BC0020480
- Hyperlipoproteinemia Type IVC0020480
- Hyperlipoproteinemia, Type IVC0020480
- Hyperlipoproteinemias, Type IVC0020480
- HyperprebetalipoproteinemiaC0020480
- Hypertriglyceridemia, FamilialC0020480
- Inducible Hyperlipemia, CarbohydrateC0020480
- Inducible Hyperlipemias, CarbohydrateC0020480
- Pure hyperglyceridaemiaC0020480
- Pure hyperglyceridemiaC0020480
- Pure hyperglyceridemia (disorder)C0020480
- Type IV HyperlipoproteinemiaC0020480
- Type IV HyperlipoproteinemiasC0020480
- Type IV hyperlipidaemiaC0020480
- Type IV hyperlipidemiaC0020480
- Type IV hyperlipoproteinaemiaC0020480
- Type IV hyperlipoproteinemiaC0020480
- Type IV lipidaemiaC0020480
- Type IV lipidemiaC0020480
- Type IV, HyperlipoproteinemiaC0020480
- Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinemiaC0020480
- endogenous hyperglyceridemiaC0020480
- endogenous hyperlipidemiaC0020480
- familial hyperlipoproteinemia type IVC0020480
- familial hyperprebetalipoproteinemiaC0020480
- familial hypertriglyceridaemiaC0020480
- familial hypertriglyceridemiaC0020480
- hyperlipidemia type ivC0020480
- type iv hyperlipidemiaC0020480
- type iv hyperlipoproteinemiaC0020480
- Elevated fasting triglyceridesC2874288
Frequently Asked Questions
What is ICD-10 code E78.1?
ICD-10-CM code E78.1 represents "Pure hyperglyceridemia". It is a billable/specific code that can be used on a claim.
Is E78.1 a billable code?
Yes, E78.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E78.1 in?
E78.1 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E78.1?
E78.1 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 4 more.
What SNOMED CT codes does E78.1 map to?
E78.1 maps to 14 SNOMED CT concepts: 129589009, 34528009, 238085009, 3744001, 302870006, and 9 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E78.1?
E78.1 is linked to 2 UMLS Concept Unique Identifiers: C0020480, C2874288. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.