E78.00
BillablePure hypercholesterolemia, unspecified
Pure hypercholesterolemia, unspecified
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Fredrickson's hyperlipoproteinemia, type IIa
- Hyperbetalipoproteinemia
- Low-density-lipoprotein-type [LDL] hyperlipoproteinemia
- (Pure) hypercholesterolemia NOS
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
- sphingolipidosis (E75.0-E75.3)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Also Known As / Clinical Terms
SNOMED CT
- High cholesterol13644009
- Hypercholesterolaemia13644009
- Hypercholesterolemia13644009
- Serum cholesterol above reference range166830008
- Serum cholesterol raised166830008
- Hyperbetalipoproteinaemia190773008
- Hyperbetalipoproteinemia190773008
- Hyperlipidaemia, group A190774002
- Hyperlipidemia, group A190774002
- Familial hyperlipoproteinaemia238038003
- Familial hyperlipoproteinemia238038003
- Primary hypercholesterolaemia238076009
- Primary hypercholesterolemia238076009
- Polygenic hypercholesterolaemia238077000
- Polygenic hypercholesterolemia238077000
- Sporadic hypercholesterolaemia238077000
- Sporadic hypercholesterolemia238077000
- Hyperalphalipoproteinaemia238080004
- Hyperalphalipoproteinemia238080004
- Pure hypercholesterolaemia267432004
- Pure hypercholesterolemia267432004
- Fredrickson type IIa hyperlipoproteinaemia397915002
- Fredrickson type IIa hyperlipoproteinemia397915002
- Essential familial hypercholesterolaemia398036000
- Essential familial hypercholesterolemia398036000
- Familial hyperbetalipoproteinaemia398036000
- Familial hyperbetalipoproteinemia398036000
- Familial hypercholesterolaemia398036000
- Familial hypercholesterolemia398036000
- LDL - Low density lipoprotein receptor disorder398036000
- LDL receptor disorder398036000
- Low density lipoprotein catabolic defect398036000
- Xanthoma due to abnormality of lipid metabolism402724009
- Hypercholesterolaemia well controlled444059002
- Hypercholesterolemia well controlled444059002
- Xanthoma due to primary hypercholesterolaemia1256075004
- Xanthoma due to primary hypercholesterolemia1256075004
UMLS
- (Pure) hypercholesterolemia NOSC0678189
- Hyperlipidaemia, group AC0678189
- Hyperlipidemia, group AC0678189
- Hyperlipidemia, group A (disorder)C0678189
- Pure hypercholesterolaemiaC0678189
- Pure hypercholesterolemiaC0678189
- Pure hypercholesterolemia (disorder)C0678189
- hypercholesterolemia pureC0678189
- pure hypercholesterolemiaC0678189
- Autosomal Dominant HypercholesterolemiaC0745103
- Autosomal Dominant HypercholesterolemiasC0745103
- Disorder, LDL ReceptorC0745103
- Disorders, LDL ReceptorC0745103
- Dominant Hypercholesterolemia, AutosomalC0745103
- Dominant Hypercholesterolemias, AutosomalC0745103
- FHCC0745103
- FHCL1C0745103
- Familial HypercholesterolemiaC0745103
- Fredrickson Type IIa hyperlipidaemiaC0745103
- Fredrickson Type IIa hyperlipidemiaC0745103
- Fredrickson Type IIa hyperlipoproteinaemiaC0745103
- Fredrickson Type IIa hyperlipoproteinemiaC0745103
- Fredrickson Type IIa lipidaemiaC0745103
- Fredrickson Type IIa lipidemiaC0745103
- Fredrickson type IIa hyperlipoproteinaemiaC0745103
- Fredrickson type IIa hyperlipoproteinemiaC0745103
- Fredrickson type IIa hyperlipoproteinemia (disorder)C0745103
- Fredrickson's hyperlipoproteinemia, type IIaC0745103
- HYPER-LOW-DENSITY-LIPOPROTEINEMIAC0745103
- HYPERCHOLESTEROLEMIA, FAMILIAL, 1C0745103
- HYPERCHOLESTEROLEMIC XANTHOMATOSIS, FAMILIALC0745103
- HYPERLIPOPROTEINEMIA, TYPE IIC0745103
- HYPERLIPOPROTEINEMIA, TYPE IIAC0745103
- Hypercholesterolemia, Autosomal DominantC0745103
- Hypercholesterolemias, Autosomal DominantC0745103
- Hyperlipidemia Type IIaC0745103
- Hyperlipoproteinemia Type IIaC0745103
- Hyperlipoproteinemia Type IIasC0745103
- Hyperlipoproteinemia, Type IIaC0745103
- Hyperlipoproteinemias, Type IIaC0745103
- LDL RECEPTOR DISORDERC0745103
- LDL Receptor DisorderC0745103
- LDL Receptor DisordersC0745103
- Receptor Disorder, LDLC0745103
- Receptor Disorders, LDLC0745103
- Type IIa HyperlipidemiaC0745103
- Type IIa HyperlipoproteinemiaC0745103
- Type IIa HyperlipoproteinemiasC0745103
- Type IIa hyperlipidaemiaC0745103
- Type IIa hyperlipidemiaC0745103
- Type IIa hyperlipoproteinaemiaC0745103
- Type IIa hyperlipoproteinemiaC0745103
- HyperbetalipoproteinemiaC4270821
- Low-density-lipoprotein-type [LDL] hyperlipoproteinemiaC4270821
- Pure hypercholesterolemia, unspecifiedC4268183
Frequently Asked Questions
What is the ICD-10 code for pure hypercholesterolemia, unspecified?
The ICD-10-CM code for pure hypercholesterolemia, unspecified is E78.00. The full clinical description is "Pure hypercholesterolemia, unspecified". E78.00 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E78.00 mean?
ICD-10-CM code E78.00 represents "Pure hypercholesterolemia, unspecified". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E78.00 a billable code?
Yes, E78.00 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E78.00 in?
E78.00 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E78.00?
E78.00 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 4 more.
What SNOMED CT codes does E78.00 map to?
E78.00 maps to 14 SNOMED CT concepts: 398036000, 238038003, 397915002, 13644009, 238080004, and 9 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E78.00?
E78.00 is linked to 4 UMLS Concept Unique Identifiers: C0678189, C0745103, C4270821, C4268183. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.