C49.9
BillableMalignant neoplasm of connective and soft tissue, unsp
Malignant neoplasm of connective and soft tissue, unspecified
Coding Notes
Includes
Conditions included under this code
- malignant neoplasm of blood vessel
- malignant neoplasm of bursa
- malignant neoplasm of cartilage
- malignant neoplasm of fascia
- malignant neoplasm of fat
- malignant neoplasm of ligament, except uterine
- malignant neoplasm of lymphatic vessel
- malignant neoplasm of muscle
- malignant neoplasm of synovia
- malignant neoplasm of tendon (sheath)
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- Kaposi's sarcoma of soft tissue (C46.1)
- malignant neoplasm of heart (C38.0)
- malignant neoplasm of peripheral nerves and autonomic nervous system (C47.-)
- malignant neoplasm of peritoneum (C48.2)
- malignant neoplasm of retroperitoneum (C48.0)
- malignant neoplasm of uterine ligament (C57.3)
- mesothelioma (C45.-)
Also Known As / Clinical Terms
SNOMED CT
- Primary malignant neoplasm of blood vessel93714009
- Primary malignant neoplasm of muscle93913006
- Skin tumor of smooth muscle origin254765000
- Skin tumour of smooth muscle origin254765000
- Cutaneous leiomyosarcoma254771006
- Liposarcoma254829001
- Malignant lipomatous tumor254829001
- Malignant lipomatous tumour254829001
- Sarcoma of bone and connective tissue255067005
- Malignant neoplasm of dermis255096006
- Malignant tumor of dermis255096006
- Malignant tumour of dermis255096006
- Malignant neoplasm of soft tissue269469005
- Malignant tumor of soft tissue269469005
- Malignant tumour of soft tissue269469005
- Malignant neoplasm of bone, connective tissue, skin and breast271467005
- Malignant neoplasm of fibrous tissue276797002
- Malignant tumor of fibrous tissue276797002
- Malignant tumour of fibrous tissue276797002
- Rhabdomyosarcoma302847003
- Rhabdosarcoma302847003
- Malignant synovioma302851001
- Synovial sarcoma302851001
- Local recurrence of malignant neoplasm of soft tissue314974009
- Local recurrence of malignant tumor of soft tissue314974009
- Local recurrence of malignant tumour of soft tissue314974009
- Cancer of muscle363495004
- Malignant neoplasm of muscle363495004
- Malignant tumor of muscle363495004
- Malignant tumour of muscle363495004
- Vaccine-induced fibrosarcoma370511006
- Primary malignant neoplasm of soft tissues372010005
- Pleomorphic malignant fibrous histiocytoma of skin398903003
- Myxofibrosarcoma of skin400175006
- Myxoid malignant fibrous histiocytoma of skin400175006
- Clear cell sarcoma402561003
- Malignant melanoma of soft tissues402561003
- Malignant neoplasm of subcutaneous fibrous tissue402871009
- Angiosarcoma403977003
- Haemangioendothelioma403980002
- Hemangioendothelioma403980002
- Epithelioid haemangioendothelioma403981003
- Epithelioid hemangioendothelioma403981003
- Intravascular angiosarcoma403985007
- Lymphangiosarcoma403986008
- Infantile fibrosarcoma403996004
- Malignant infantile fibrosarcoma403996004
- Malignant fibrous histiocytoma of skin404014008
- Superficial malignant fibrous histiocytoma of skin404015009
- Giant cell malignant fibrous histiocytoma of skin404016005
- Inflammatory malignant fibrous histiocytoma of skin404017001
- Malignant granular cell tumor404041003
- Malignant granular cell tumour404041003
- Epithelioid leiomyosarcoma of skin404045007
- Myxoid leiomyosarcoma of skin404046008
- Cutaneous leiomyosarcoma with granular cell change404047004
- Embryonal rhabdomyosarcoma404051002
- Botryoid rhabdomyosarcoma404052009
- Sarcoma botryoides404052009
- Alveolar rhabdomyosarcoma404053004
- Pleomorphic rhabdomyosarcoma404054005
- Spindle cell rhabdomyosarcoma404055006
- Alveolar soft part sarcoma404056007
- Adipocytic liposarcoma404067008
- Sclerosing liposarcoma404068003
- Myxoid liposarcoma404069006
- Pleomorphic liposarcoma404071006
- Dedifferentiated liposarcoma404072004
- Spindle cell liposarcoma404073009
- Extraskeletal osteosarcoma404077005
- Chondroid sarcoma404079008
- Extraskeletal myxoid chondrosarcoma404079008
- Low-grade fibromyxoid sarcoma404088004
- Surgical margin uninvolved by sarcoma405911005
- Surgical margin involved by sarcoma405912003
- Surgical margin involvement by sarcoma cannot be assessed405914002
- Intergroup rhabdomyosarcoma study post-surgical clinical group finding405917009
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIA: Localised or locally extensive tumour, gross residual disease after biopsy only405962008
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIA: Localized or locally extensive tumor, gross residual disease after biopsy only405962008
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIB: Localised or locally extensive tumour, gross residual disease after major resection (greater than 50 percent debulking)405963003
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIB: Localised or locally extensive tumour, gross residual disease after major resection (greater than 50% debulking)405963003
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIB: Localized or locally extensive tumor, gross residual disease after major resection (greater than 50 percent debulking)405963003
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIB: Localized or locally extensive tumor, gross residual disease after major resection (greater than 50% debulking)405963003
- Intergroup rhabdomyosarcoma study post-surgical clinical group IV: Any size primary tumor, with or without regional lymph node involvement, with distant metastases, without respect to surgical approach to primary tumor405964009
- Intergroup rhabdomyosarcoma study post-surgical clinical group IV: Any size primary tumour, with or without regional lymph node involvement, with distant metastases, without respect to surgical approach to primary tumour405964009
- Primary leiomyosarcoma423807009
- Sarcoma424413001
- Sarcoma of soft tissue424952003
- Malignant fibromatous neoplasm443250000
- Malignant fibrous histiocytoma443439001
- Leiomyosarcoma443719001
- Leiomyosarcoma of connective tissue447804006
- Ewing sarcoma of soft tissue447951009
- Ewing's sarcoma of soft tissue447951009
- Fibrosarcoma of connective tissue448139005
- Malignant neoplasm of connective tissue448274000
- Liposarcoma of connective tissue448554008
- Sarcoma of connective tissue449293008
- Primary liposarcoma of soft tissue of limb721577002
- Primary synovial sarcoma of soft tissue of limb721579004
- Primary myxofibrosarcoma723076008
- Epithelioid sarcoma782827000
- Extraskeletal myxoid chondrosarcoma of soft tissue of limb860832001
- DSRCT - desmoplastic small round cell tumor1156420003
- DSRCT - desmoplastic small round cell tumour1156420003
- Desmoplastic small round cell tumor1156420003
- Desmoplastic small round cell tumour1156420003
- Metastatic sarcoma of retroperitoneum1251498002
- Metastatic sarcoma to retroperitoneum1251498002
- Secondary sarcoma of retroperitoneum1251498002
- Malignant neoplasm of blood vessel1254957001
- Primary fibrosarcoma of connective tissue1259453005
- Primary botryoid rhabdomyosarcoma1259582008
- Primary sarcoma botryoides1259582008
- Primary spindle cell rhabdomyosarcoma1259583003
- Primary extraskeletal osteosarcoma1259585005
- Primary malignant granular cell tumor1259785007
- Primary malignant granular cell tumour1259785007
- Primary malignant synovioma1268484002
- Primary synovial sarcoma1268484002
- Primary alveolar soft part sarcoma1268531004
- Primary Ewing sarcoma of soft tissue1268534007
- Primary Ewing's sarcoma of soft tissue1268534007
- Primary epithelioid sarcoma1268547002
- Primary malignant fibrous histiocytoma1268715005
- Primary epithelioid haemangioendothelioma1268904009
- Primary epithelioid hemangioendothelioma1268904009
- Primary desmoplastic small round cell tumor1269044006
- Primary desmoplastic small round cell tumour1269044006
- Metastatic rhabdomyosarcoma1269121005
- Metastatic rhabdosarcoma1269121005
- Metastatic embryonal rhabdomyosarcoma1279882001
- Undifferentiated pleomorphic sarcoma1290751005
- Undifferentiated round cell sarcoma1290803006
- Undifferentiated spindle cell sarcoma1290807007
- Myxoid pleomorphic liposarcoma1290810000
- Classic epithelioid sarcoma1290825000
- Well differentiated liposarcoma1290827008
- Low grade myofibroblastic sarcoma1290828003
- Sclerosing epithelioid fibrosarcoma1290851003
- Fibrosarcoma1290852005
- Epithelioid myxofibrosarcoma1290855007
- Intimal sarcoma1290865001
- Large cell epithelioid sarcoma1290886001
- Proximal epithelioid sarcoma1290886001
- Anaplastic embryonal rhabdomyosarcoma1290888000
- Spindle cell synovial sarcoma1290889008
- Biphasic synovial sarcoma1290890004
- Poorly differentiated synovial sarcoma1290891000
- Epithelioid liposarcoma1290895009
- Inflammatory liposarcoma1290901007
- Myxoinflammatory fibroblastic sarcoma1290902000
- Undifferentiated sarcoma1290903005
- Malignant ossifying fibromyxoid tumor1292988006
- Malignant ossifying fibromyxoid tumour1292988006
- Malignant solitary fibrous tumor1292990007
- Malignant solitary fibrous tumour1292990007
- Lipoma-like liposarcoma1293066000
- Ectomesenchymoma1295216003
- Rhabdomyosarcoma with ganglionic differentiation1295216003
- Malignant tenosynovial giant cell tumor1295242003
- Malignant tenosynovial giant cell tumour1295242003
- Malignant phosphaturic mesenchymal tumor1295266009
- Malignant phosphaturic mesenchymal tumour1295266009
- Metastatic spindle cell rhabdomyosarcoma1336170004
- Metastatic spindle cell rhabdosarcoma1336170004
- Metastatic malignant synovioma1336171000
- Metastatic synovial sarcoma1336171000
- Metastatic fibrosarcoma1336176005
- Metastatic myxofibrosarcoma1336182008
- Metastatic pleomorphic rhabdomyosarcoma1336185005
- Metastatic infantile fibrosarcoma1339049006
- Metastatic malignant infantile fibrosarcoma1339049006
Frequently Asked Questions
What is ICD-10 code C49.9?
ICD-10-CM code C49.9 represents "Malignant neoplasm of connective and soft tissue, unspecified". It is a billable/specific code that can be used on a claim.
Is C49.9 a billable code?
Yes, C49.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is C49.9 in?
C49.9 is in Chapter 2: Neoplasms (codes C00-D49).
What codes cannot be used with C49.9?
C49.9 has Excludes1 notes indicating codes that cannot be used together with it, including: malignant neoplasm of cartilage (of):; articular (C40-C41); larynx (C32.3); and 2 more.
What SNOMED CT codes does C49.9 map to?
C49.9 maps to 122 SNOMED CT concepts: 404067008, 404053004, 404056007, 1290888000, 403977003, and 117 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for C49.9?
C49.9 is linked to 1 UMLS Concept Unique Identifier: C0348362. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.