Chapter 3: Diseases of the Blood and Blood-Forming Organs
ICD-10 to ICD-11 crosswalk mappings for codes D50-D89
192 ICD-10 codes in this chapter have ICD-11 crosswalk mappings from the WHO.
Covers anemia (iron deficiency, sickle cell, aplastic), coagulation disorders including hemophilia and thrombocytopenia, immune deficiencies, and other blood disorders. Iron deficiency anemia (D50) and other anemias are among the most frequently coded conditions in this chapter.
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D50-D53: Nutritional Anemias
23 codes with ICD-11 mappings
D50Iron deficiency anemia1 mappingD50.0Iron deficiency anemia secondary to blood loss (chronic)1 mappingD50.1Sideropenic dysphagia1 mappingD50.8Other iron deficiency anemias1 mappingD50.9Iron deficiency anemia, unspecified1 mappingD51Vitamin B12 deficiency anemia1 mappingD51.0Vitamin B12 defic anemia due to intrinsic factor deficiency1 mappingD51.1Vit B12 defic anemia d/t slctv vit B12 malabsorp w protein1 mappingD51.2Transcobalamin II deficiency1 mappingD51.3Other dietary vitamin B12 deficiency anemia1 mappingD51.8Other vitamin B12 deficiency anemias1 mappingD51.9Vitamin B12 deficiency anemia, unspecified1 mappingD52Folate deficiency anemia1 mappingD52.0Dietary folate deficiency anemia1 mappingD52.1Drug-induced folate deficiency anemia1 mappingD52.8Other folate deficiency anemias1 mappingD52.9Folate deficiency anemia, unspecified1 mappingD53Other nutritional anemias1 mappingD53.0Protein deficiency anemia1 mappingD53.1Other megaloblastic anemias, not elsewhere classified1 mappingD53.2Scorbutic anemia1 mappingD53.8Other specified nutritional anemias1 mappingD53.9Nutritional anemia, unspecified1 mapping
D55-D59: Hemolytic Anemias
37 codes with ICD-11 mappings
D55Anemia due to enzyme disorders1 mappingD55.0Anemia due to glucose-6-phosphate dehydrogenase deficiency1 mappingD55.1Anemia due to other disorders of glutathione metabolism1 mappingD55.2Anemia due to disorders of glycolytic enzymes1 mappingD55.3Anemia due to disorders of nucleotide metabolism1 mappingD55.8Other anemias due to enzyme disorders1 mappingD55.9Anemia due to enzyme disorder, unspecified1 mappingD56Thalassemia1 mappingD56.0Alpha thalassemia1 mappingD56.1Beta thalassemia1 mappingD56.2Delta-beta thalassemia1 mappingD56.3Thalassemia minor1 mappingD56.4Hereditary persistence of fetal hemoglobin [HPFH]1 mappingD56.8Other thalassemias1 mappingD56.9Thalassemia, unspecified1 mappingD57Sickle-cell disorders1 mappingD57.0Hb-SS disease with crisis1 mappingD57.1Sickle-cell disease without crisis1 mappingD57.2Sickle-cell/Hb-C disease1 mappingD57.3Sickle-cell trait1 mappingD57.8Other sickle-cell disorders1 mappingD58Other hereditary hemolytic anemias1 mappingD58.0Hereditary spherocytosis1 mappingD58.1Hereditary elliptocytosis1 mappingD58.2Other hemoglobinopathies1 mappingD58.8Other specified hereditary hemolytic anemias1 mappingD58.9Hereditary hemolytic anemia, unspecified1 mappingD59Acquired hemolytic anemia1 mappingD59.0Drug-induced autoimmune hemolytic anemia1 mappingD59.1Other autoimmune hemolytic anemias1 mappingD59.2Drug-induced nonautoimmune hemolytic anemia1 mappingD59.3Hemolytic-uremic syndrome1 mappingD59.4Other nonautoimmune hemolytic anemias1 mappingD59.5Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]1 mappingD59.6Hemoglobinuria due to hemolysis from other external causes1 mappingD59.8Other acquired hemolytic anemias1 mappingD59.9Acquired hemolytic anemia, unspecified1 mapping
D60-D64: Aplastic and Other Anemias and Other Bone Marrow Failure Syndromes
24 codes with ICD-11 mappings
D60Acquired pure red cell aplasia [erythroblastopenia]1 mappingD60.0Chronic acquired pure red cell aplasia1 mappingD60.1Transient acquired pure red cell aplasia1 mappingD60.8Other acquired pure red cell aplasias1 mappingD60.9Acquired pure red cell aplasia, unspecified1 mappingD61Oth aplastic anemias and other bone marrow failure syndromes1 mappingD61.0Constitutional aplastic anemia1 mappingD61.1Drug-induced aplastic anemia1 mappingD61.2Aplastic anemia due to other external agents1 mappingD61.3Idiopathic aplastic anemia1 mappingD61.8Oth aplastic anemias and other bone marrow failure syndromes1 mappingD61.9Aplastic anemia, unspecified1 mappingD62Acute posthemorrhagic anemia1 mappingD63Anemia in chronic diseases classified elsewhere1 mappingD63.0Anemia in neoplastic disease1 mappingD63.8Anemia in other chronic diseases classified elsewhere1 mappingD64Other anemias1 mappingD64.0Hereditary sideroblastic anemia1 mappingD64.1Secondary sideroblastic anemia due to disease1 mappingD64.2Secondary sideroblastic anemia due to drugs and toxins1 mappingD64.3Other sideroblastic anemias1 mappingD64.4Congenital dyserythropoietic anemia1 mappingD64.8Other specified anemias1 mappingD64.9Anemia, unspecified1 mapping
D65-D69: Coagulation Defects, Purpura and Other Hemorrhagic Conditions
23 codes with ICD-11 mappings
D65Disseminated intravascular coagulation1 mappingD66Hereditary factor VIII deficiency1 mappingD67Hereditary factor IX deficiency1 mappingD68Other coagulation defects1 mappingD68.0Von Willebrand disease1 mappingD68.1Hereditary factor XI deficiency1 mappingD68.2Hereditary deficiency of other clotting factors1 mappingD68.3Hemorrhagic disorder due to circulating anticoagulants1 mappingD68.4Acquired coagulation factor deficiency1 mappingD68.5Primary thrombophilia1 mappingD68.6Other thrombophilia1 mappingD68.8Other specified coagulation defects1 mappingD68.9Coagulation defect, unspecified1 mappingD69Purpura and other hemorrhagic conditions1 mappingD69.0Allergic purpura1 mappingD69.1Qualitative platelet defects1 mappingD69.2Other nonthrombocytopenic purpura1 mappingD69.3Immune thrombocytopenic purpura1 mappingD69.4Other primary thrombocytopenia1 mappingD69.5Secondary thrombocytopenia1 mappingD69.6Thrombocytopenia, unspecified1 mappingD69.8Other specified hemorrhagic conditions1 mappingD69.9Hemorrhagic condition, unspecified1 mapping
D70-D77: Other Disorders of Blood and Blood-Forming Organs
30 codes with ICD-11 mappings
D70Neutropenia1 mappingD71Functional disorders of polymorphonuclear neutrophils1 mappingD72Other disorders of white blood cells1 mappingD72.0Genetic anomalies of leukocytes1 mappingD72.1Eosinophilia1 mappingD72.8Other specified disorders of white blood cells1 mappingD72.9Disorder of white blood cells, unspecified1 mappingD73Diseases of spleen1 mappingD73.0Hyposplenism1 mappingD73.1Hypersplenism1 mappingD73.2Chronic congestive splenomegaly1 mappingD73.3Abscess of spleen1 mappingD73.4Cyst of spleen1 mappingD73.5Infarction of spleen1 mappingD73.8Other diseases of spleen1 mappingD73.9Disease of spleen, unspecified1 mappingD74Methemoglobinemia1 mappingD74.0Congenital methemoglobinemia1 mappingD74.8Other methemoglobinemias1 mappingD74.9Methemoglobinemia, unspecified1 mappingD75Other and unsp diseases of blood and blood-forming organs1 mappingD75.0Familial erythrocytosis1 mappingD75.1Secondary polycythemia1 mappingD75.8Other specified diseases of blood and blood-forming organs1 mappingD75.9Disease of blood and blood-forming organs, unspecified1 mappingD76Oth dis with lymphoreticular and reticulohistiocytic tissue1 mappingD76.1Hemophagocytic lymphohistiocytosis1 mappingD76.2Hemophagocytic syndrome, infection-associated1 mappingD76.3Other histiocytosis syndromes1 mappingD77Oth disord of bld/bld-frm organs in diseases classd elswhr1 mapping
D80-D89: Certain Disorders Involving the Immune Mechanism
55 codes with ICD-11 mappings
D80Immunodeficiency with predominantly antibody defects1 mappingD80.0Hereditary hypogammaglobulinemia1 mappingD80.1Nonfamilial hypogammaglobulinemia1 mappingD80.2Selective deficiency of immunoglobulin A [IgA]1 mappingD80.3Selective deficiency of immunoglobulin G [IgG] subclasses1 mappingD80.4Selective deficiency of immunoglobulin M [IgM]1 mappingD80.5Immunodeficiency with increased immunoglobulin M [IgM]1 mappingD80.6Antibody defic w near-norm immunoglob or w hyperimmunoglob1 mappingD80.7Transient hypogammaglobulinemia of infancy1 mappingD80.8Other immunodeficiencies with predominantly antibody defects1 mappingD80.9Immunodeficiency with predominantly antibody defects, unsp1 mappingD81Combined immunodeficiencies1 mappingD81.0Severe combined immunodeficiency with reticular dysgenesis1 mappingD81.1Severe combined immunodeficiency w low T- and B-cell numbers1 mappingD81.2Severe combined immunodef w low or normal B-cell numbers1 mappingD81.3Adenosine deaminase [ADA] deficiency1 mappingD81.4Nezelof's syndrome1 mappingD81.5Purine nucleoside phosphorylase [PNP] deficiency1 mappingD81.6Major histocompatibility complex class I deficiency1 mappingD81.7Major histocompatibility complex class II deficiency1 mappingD81.8Other combined immunodeficiencies1 mappingD81.9Combined immunodeficiency, unspecified1 mappingD82Immunodeficiency associated with other major defects1 mappingD82.0Wiskott-Aldrich syndrome1 mappingD82.1Di George's syndrome1 mappingD82.2Immunodeficiency with short-limbed stature1 mappingD82.3Immunodef fol heredit defctv response to Epstein-Barr virus1 mappingD82.4Hyperimmunoglobulin E [IgE] syndrome1 mappingD82.8Immunodeficiency associated with oth major defects1 mappingD82.9Immunodeficiency associated with major defect, unspecified1 mappingD83Common variable immunodeficiency1 mappingD83.0Com variab immunodef w predom abnlt of B-cell nums & functn1 mappingD83.1Com variab immunodef w predom immunoreg T-cell disorders1 mappingD83.2Common variable immunodef w autoantibodies to B- or T-cells1 mappingD83.8Other common variable immunodeficiencies1 mappingD83.9Common variable immunodeficiency, unspecified1 mappingD84Other immunodeficiencies1 mappingD84.0Lymphocyte function antigen-1 [LFA-1] defect1 mappingD84.1Defects in the complement system1 mappingD84.8Other specified immunodeficiencies1 mappingD84.9Immunodeficiency, unspecified1 mappingD86Sarcoidosis1 mappingD86.0Sarcoidosis of lung1 mappingD86.1Sarcoidosis of lymph nodes1 mappingD86.2Sarcoidosis of lung with sarcoidosis of lymph nodes1 mappingD86.3Sarcoidosis of skin1 mappingD86.8Sarcoidosis of other sites1 mappingD86.9Sarcoidosis, unspecified1 mappingD89Oth disorders involving the immune mechanism, NEC1 mappingD89.0Polyclonal hypergammaglobulinemia1 mappingD89.1Cryoglobulinemia1 mappingD89.2Hypergammaglobulinemia, unspecified1 mappingD89.3Immune reconstitution syndrome1 mappingD89.8Oth disrd involving the immune mechanism, NEC1 mappingD89.9Disorder involving the immune mechanism, unspecified1 mapping