Q87.89

Billable

Oth congenital malformation syndromes, NEC

Other specified congenital malformation syndromes, not elsewhere classified

Coding Notes

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

  • inborn errors of metabolism (E70-E88)

Use Additional Code

Additional codes that should follow this code

  • code(s) to identify all associated manifestations

Also Known As / Clinical Terms

SNOMED CT

Frequently Asked Questions

What is the ICD-10 code for oth congenital malformation syndromes, nec?

The ICD-10-CM code for oth congenital malformation syndromes, nec is Q87.89. The full clinical description is "Other specified congenital malformation syndromes, not elsewhere classified". Q87.89 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q87.89 mean?

ICD-10-CM code Q87.89 represents "Other specified congenital malformation syndromes, not elsewhere classified". It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q87.89 a billable code?

Yes, Q87.89 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q87.89 in?

Q87.89 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What codes cannot be used with Q87.89?

Q87.89 has Excludes1 notes indicating codes that cannot be used together with it, including: Zellweger syndrome (E71.510).

Are additional codes required with Q87.89?

Yes, when using Q87.89 you should also code: code(s) to identify all associated manifestations.

What SNOMED CT codes does Q87.89 map to?

Q87.89 maps to 219 SNOMED CT concepts: 4135001, 880078001, 880081006, 880086001, 303098002, and 214 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q87.89?

Q87.89 is linked to 1 UMLS Concept Unique Identifier: C0869083. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

Automate ICD-10 Coding With AI

Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.

Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.