Q03.9
BillableCongenital hydrocephalus, unspecified
Congenital hydrocephalus, unspecified
Status
Billable / Specific
Parent Code
Q03Coding Notes
Includes
Conditions included under this code
- hydrocephalus in newborn
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- Arnold-Chiari syndrome, type II (Q07.0-)
- acquired hydrocephalus (G91.-)
- hydrocephalus due to congenital toxoplasmosis (P37.1)
- hydrocephalus with spina bifida (Q05.0-Q05.4)
Excludes 2
Conditions not included here, but the patient may have both
- inborn errors of metabolism (E70-E88)
Also Known As / Clinical Terms
SNOMED CT
- Arrested hydrocephalus4113009
- Macroencephaly9740002
- Megalencephaly9740002
- Dandy-Walker deformity14447001
- Dandy-Walker malformation14447001
- Dandy-Walker syndrome14447001
- Aqueduct of Sylvius anomaly25397008
- Congenital abnormality of sclera32809005
- Congenital anomaly of sclera32809005
- Congenital dilatation of cerebral ventricles47032000
- Congenital hydrencephalus47032000
- Congenital hydrencephaly47032000
- Congenital hydrocephalus47032000
- Congenital hydrocephaly47032000
- Hydrocephalus in newborn47032000
- Primary hydrocephalus47032000
- Primary hydrocephaly47032000
- Congenital stenosis of aqueduct of Sylvius50429003
- EFE - Endocardial fibroelastosis65457005
- Elastomyofibrosis65457005
- Endocardial fibroelastosis65457005
- Congenital humpback71311003
- Congenital hunchback71311003
- Congenital kyphosis71311003
- Bickers-Adams syndrome71779008
- X-linked hydrocephalus71779008
- X-linked hydrocephalus syndrome71779008
- Congenital elevation of scapula79120002
- Sprengel's deformity79120002
- Undescended shoulder79120002
- CSF - Cerebrospinal rhinorrhea85638002
- CSF - Cerebrospinal rhinorrhoea85638002
- Cerebrospinal fluid rhinorrhea85638002
- Cerebrospinal fluid rhinorrhoea85638002
- Cerebrospinal rhinorrhea85638002
- Cerebrospinal rhinorrhoea85638002
- Internal hydrocephalus128431009
- Cerebral degeneration due to congenital hydrocephalus192814005
- Hypoplasia of corpus callosum204043002
- Abnormal blue sclerae204164000
- Blue sclera204164000
- Hydrocephalus230745008
- Hydrocephaly230745008
- Obstructive hydrocephalus230746009
- Android fat distribution248311001
- Central obesity248311001
- Centripetal obesity248311001
- Fat body with thin limbs248311001
- Obesity of face and trunk, sparing limbs248311001
- Truncal obesity248311001
- External hydrocephalus253132009
- Agenesis of cerebellum253172000
- Congenital absence of cerebellum253172000
- Total agenesis of cerebellum253172000
- Congenital anomaly of the meninges253199003
- Congenital malformation of the meninges253199003
- Congenital deformity of lumbosacral region254033007
- Kyphosis deformity of thoracic spine298493002
- Kyphosis of dorsal spine298493002
- Kyphosis of thoracic spine298493002
- Hydrocephalus associated with congenital aqueduct stenosis302882002
- Naevus flammeus416377005
- Nevus flammeus416377005
- PWS - Port-wine stain416377005
- Port wine stain of skin416377005
- Port-wine birthmark416377005
- Port-wine naevus416377005
- Port-wine nevus416377005
- Port-wine stain416377005
- Port-wine stain of skin416377005
- Portwine naevus416377005
- Portwine nevus416377005
- Mega cisterna magna447739003
- Agenesis of cerebellum and hydrocephalus syndrome715990006
- Cerebellum agenesis with hydrocephaly715990006
- Game Friedman Paradice syndrome716198008
- Growth delay with hydrocephalus and lung hypoplasia syndrome716198008
- CRASH syndrome716996008
- Hypoplasia of corpus callosum and mental retardation with adducted thumbs and spasticity and hydrocephalus syndrome716996008
- Hypoplasia of corpus callosum, intellectual disability, adducted thumbs, spasticity, hydrocephalus syndrome716996008
- L1 syndrome716996008
- Beemer Ertbruggen syndrome717859007
- Beemer lethal malformation syndrome717859007
- Hydrocephalus, cardiac malformation, dense bone syndrome717859007
- VACTERL syndrome with hydrocephalus719043002
- Vertebral abnormality, anal atresia, cardiac abnormality, tracheo-esophageal fistula, renal anomaly, limb defect syndrome with hydrocephalus719043002
- Vertebral abnormality, anal atresia, cardiac abnormality, tracheo-oesophageal fistula, renal anomaly, limb defect syndrome with hydrocephalus719043002
- Braddock Jones Superneau syndrome720813007
- Craniosynostosis with Dandy-Walker malformation and hydrocephalus syndrome720813007
- HEC (hydrocephalus, endocardial fibroelastosis, cataract) syndrome721015008
- HEC syndrome721015008
- Hydrocephalus with endocardial fibroelastosis and cataract syndrome721015008
- Ferlini Ragno Calzolari syndrome721229003
- Hydrocephalus, costovertebral dysplasia, Sprengel anomaly syndrome721229003
- Waaler Aarskog syndrome721229003
- Hydrocephalus with obesity and hypogonadism syndrome721231007
- Sengers Hamel Otten syndrome721231007
- MPPH (megalencephaly, polymicrogyria, polydactyly, hydrocephalus) syndrome722036008
- MPPH syndrome722036008
- Megalencephaly, polymicrogyria, postaxial polydactyly, hydrocephalus syndrome722036008
- Daish Hardman Lamont syndrome732926009
- Hydrocephalus, tall stature, joint laxity syndrome732926009
- Hydrocephaly, tall stature, joint laxity syndrome732926009
- Congenital obstructive hydrocephalus762295002
- Daentl Townsend Siegel syndrome773280009
- Hydrocephalus, blue sclera, nephropathy syndrome773280009
- Thoracic dysplasia and hydrocephalus syndrome782951006
- Nova syndrome783701002
- Port-wine naevi, mega cisterna magna, hydrocephalus syndrome783701002
- Port-wine nevi, mega cisterna magna, hydrocephalus syndrome783701002
- Congenital endocardial fibroelastosis1141882007
- Fibroelastosis cordis1141882007
- Congenital hypoplasia of cerebral hemisphere1144337000
- Hemispheric cerebral hypoplasia1144337000
- Congenital hypoplasia of cerebral white matter1144343003
- Congenital hydrocephalus, low insertion of umbilicus syndrome1208346003
- Palmer Pagon syndrome1208346003
- Cerebrospinal fluid rhinorrhea due to hydrocephalus1259109009
- Cerebrospinal fluid rhinorrhoea due to hydrocephalus1259109009
- Cranial cerebrospinal fluid leak due to hydrocephalus1259542001
- Leak of cranial cerebrospinal fluid due to hydrocephalus1259542001
- Cranial cerebrospinal fluid fistula1259545004
- Cranial cerebrospinal fluid leak1259545004
- Leak of cranial cerebrospinal fluid1259545004
- Congenital kyphosis of thoracic spine305141000119101
UMLS
- CONGEN HYDROCEPHALUSC0020256
- Congenital HydrocephalusC0020256
- Congenital dilatation of cerebral ventriclesC0020256
- Congenital hydrencephalusC0020256
- Congenital hydrencephalyC0020256
- Congenital hydrocephalusC0020256
- Congenital hydrocephalus (disorder)C0020256
- Congenital hydrocephalus, unspecifiedC0020256
- Congenital hydrocephalyC0020256
- Hydrocephalus congenitalC0020256
- Hydrocephalus in newbornC0020256
- Hydrocephalus, CongenitalC0020256
- Hydrocephalus, congenitalC0020256
- Primary hydrocephalusC0020256
- Primary hydrocephalyC0020256
- congenital hydrocephalusC0020256
- congenital hydrocephalyC0020256
- hydrocephalus congenitalC0020256
- hydrocephalus in newbornC0020256
Frequently Asked Questions
What is the ICD-10 code for congenital hydrocephalus, unspecified?
The ICD-10-CM code for congenital hydrocephalus, unspecified is Q03.9. The full clinical description is "Congenital hydrocephalus, unspecified". Q03.9 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q03.9 mean?
ICD-10-CM code Q03.9 represents "Congenital hydrocephalus, unspecified". It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q03.9 a billable code?
Yes, Q03.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q03.9 in?
Q03.9 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q03.9?
Q03.9 has Excludes1 notes indicating codes that cannot be used together with it, including: Arnold-Chiari syndrome, type II (Q07.0-); acquired hydrocephalus (G91.-); hydrocephalus due to congenital toxoplasmosis (P37.1); and 1 more.
What SNOMED CT codes does Q03.9 map to?
Q03.9 maps to 50 SNOMED CT concepts: 204164000, 253172000, 715990006, 248311001, 25397008, and 45 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q03.9?
Q03.9 is linked to 1 UMLS Concept Unique Identifier: C0020256. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.