E27.1
BillablePrimary adrenocortical insufficiency
Primary adrenocortical insufficiency
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Addison's disease
- Autoimmune adrenalitis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Also Known As / Clinical Terms
SNOMED CT
- Congenital Addison disease12427005
- Congenital primary adrenocortical hypofunction12427005
- Myopathy in Addison disease34253008
- Myopathy in Addison's disease34253008
- Endocrine myopathy57958006
- Muscle disease related to endocrine disease57958006
- Muscle disorders associated with endocrine disease57958006
- Hereditary adrenal unresponsiveness to corticotropin71974009
- Addison disease due to autoimmunity76715008
- Addison's disease due to autoimmunity76715008
- Autoimmune Addison's disease76715008
- Autoimmune adrenal atrophy76715008
- Autoimmune adrenalitis76715008
- CAH - Congenital adrenal hypoplasia93235007
- Congenital adrenal hypoplasia93235007
- Congenital hypoplasia of adrenal gland93235007
- Congenital small adrenal gland93235007
- Hyperpigmentation of oral mucosa235038002
- Melanin pigmentation of oral mucosa235038002
- SRNS - Steroid-resistant nephrotic syndrome236381000
- Steroid-resistant nephrotic syndrome236381000
- Steroid-unresponsive nephrotic syndrome236381000
- RTH (resistance to thyroid hormone) syndrome237559000
- Resistance to TH (thyroid hormone) syndrome237559000
- Resistance to thyroid hormone syndrome237559000
- Thyroid hormone resistance237559000
- Thyroid hormone resistance syndrome237559000
- Pituitary thyroid hormone resistance360348000
- Addison disease363732003
- Addison's disease363732003
- Primary adrenocortical insufficiency373662000
- Primary hypoadrenalism373662000
- Buccal pigmentation due to Addison disease403252006
- Buccal pigmentation due to Addison's disease403252006
- Primary immunodeficiency due to MCM4 (mini-chromosome maintenance complex component 4) deficiency724275005
- Primary immunodeficiency due to MCM4 deficiency724275005
- Primary immunodeficiency with natural killer cell deficiency and adrenal insufficiency724275005
- Melanosis of mucosa of body orifice724847001
- Mucosal melanosis724847001
- Adrenomyodystrophy763311001
- Inherited isolated adrenal insufficiency due to partial CYP11A1 deficiency764960005
- Inherited isolated adrenal insufficiency due to partial cytochrome P450 family 11 subfamily A member 1 deficiency764960005
- Familial glucocorticoid deficiency765326001
- ACTH (adrenocorticotropic hormone) resistance syndrome1156181008
- Adrenocorticotropic hormone insensitivity1156181008
- Adrenocorticotropic hormone resistance syndrome1156181008
- Adrenocorticotropin resistance syndrome1156181008
- Familial steroid-resistant nephrotic syndrome with adrenal insufficiency1187040004
- Primary adrenal insufficiency, steroid-resistant nephrotic syndrome due to SGPL1 (sphingosine-1-phosphate lyase 1) deficiency1187040004
- Primary adrenal insufficiency, steroid-resistant nephrotic syndrome due to SGPL1 deficiency1187040004
UMLS
- ADDISON DISC0001403
- ADDISON DISEASEC0001403
- ADDISONS DISC0001403
- Addison DiseaseC0001403
- Addison diseaseC0001403
- Addison's DiseaseC0001403
- Addison's diseaseC0001403
- Addison's disease (disorder)C0001403
- Addisons DiseaseC0001403
- Adrenal Insufficiency, PrimaryC0001403
- Adrenal insufficiency (Addison disease)C0001403
- Adrenocortical Insufficiencies, PrimaryC0001403
- Adrenocortical Insufficiency, PrimaryC0001403
- Chronic Primary Adrenal InsufficiencyC0001403
- Classic Addison diseaseC0001403
- Disease Addison'sC0001403
- Disease, AddisonC0001403
- Hypoadrenalism, PrimaryC0001403
- Hypoadrenalisms, PrimaryC0001403
- HypocortisolismC0001403
- Insufficiencies, Primary AdrenocorticalC0001403
- Insufficiency, Primary AdrenocorticalC0001403
- Primary Addison diseaseC0001403
- Primary Adrenal InsufficiencyC0001403
- Primary Adrenocortical InsufficienciesC0001403
- Primary Adrenocortical InsufficiencyC0001403
- Primary HypoadrenalismC0001403
- Primary adrenocortical insufficiencyC0001403
- addison diseaseC0001403
- addison's diseaseC0001403
- primary adrenal insufficiencyC0001403
- Addison disease due to autoimmunityC0271737
- Addison's disease due to autoimmunityC0271737
- Addison's disease due to autoimmunity (disorder)C0271737
- Autoimmune Addison diseaseC0271737
- Autoimmune Addison's DiseaseC0271737
- Autoimmune Addison's diseaseC0271737
- Autoimmune AdrenalitisC0271737
- Autoimmune Primary Adrenal InsufficiencyC0271737
- Autoimmune adrenal atrophyC0271737
- Autoimmune adrenalitisC0271737
- adrenalitisC0271737
- autoimmune addison's diseaseC0271737
- autoimmune adrenalitisC0271737
- Primary adrenal insufficiencyC5848257
- Primary adrenocortical failureC5848257
- Primary adrenocortical insufficiency (disorder)C5848257
- Primary hypoadrenalismC5848257
Frequently Asked Questions
What is ICD-10 code E27.1?
ICD-10-CM code E27.1 represents "Primary adrenocortical insufficiency". It is a billable/specific code that can be used on a claim.
Is E27.1 a billable code?
Yes, E27.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E27.1 in?
E27.1 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E27.1?
E27.1 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); galactorrhea (N64.3); gynecomastia (N62); and 4 more.
What SNOMED CT codes does E27.1 map to?
E27.1 maps to 20 SNOMED CT concepts: 1156181008, 363732003, 76715008, 763311001, 403252006, and 15 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E27.1?
E27.1 is linked to 3 UMLS Concept Unique Identifiers: C0001403, C0271737, C5848257. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.