A81.0
Non-billableCreutzfeldt-Jakob disease
Creutzfeldt-Jakob disease
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Includes
Conditions included under this code
- diseases generally recognized as communicable or transmissible
- diseases of the central nervous system caused by prions
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Use Additional Code
Additional codes that should follow this code
- code to identify resistance to antimicrobial drugs (Z16.-)
- code, if applicable, to identify:
- dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
- dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
- dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
- dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
- dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
- mild neurocognitive disorder due to known physiological condition (F06.7-)
Child Codes (3)
Also Known As / Clinical Terms
UMLS
- CJ diseaseC0022336
- CJDC0022336
- CJD (Creutzfeldt Jakob Disease)C0022336
- CJD (Creutzfeldt Jakob disease)C0022336
- CJD (Creutzfeldt-Jakob Disease)C0022336
- CJD - Creutzfeldt-Jakob diseaseC0022336
- CJD CREUTZFELDT JAKOB DISC0022336
- CREUTZFELDT JAKOB DISC0022336
- CREUTZFELDT-JAKOB DISEASEC0022336
- Creutzfeld-Jacob diseaseC0022336
- Creutzfeld-Jakob diseaseC0022336
- Creutzfeldt Jacob DiseaseC0022336
- Creutzfeldt Jakob DiseaseC0022336
- Creutzfeldt Jakob SyndromeC0022336
- Creutzfeldt Jakob diseaseC0022336
- Creutzfeldt-Jacob DiseaseC0022336
- Creutzfeldt-Jakob DiseaseC0022336
- Creutzfeldt-Jakob SyndromeC0022336
- Creutzfeldt-Jakob diseaseC0022336
- Creutzfeldt-Jakob disease, unspecifiedC0022336
- Disease, Creutzfeldt JacobC0022336
- Disease, Creutzfeldt-JakobC0022336
- Disease, Jakob-CreutzfeldtC0022336
- Encephalopathies, Subacute SpongiformC0022336
- Encephalopathy, Subacute SpongiformC0022336
- JAKOB CREUTZFELDT DISC0022336
- JCD - Jakob-Creutzfeldt diseaseC0022336
- Jacob Disease, CreutzfeldtC0022336
- Jacob-Creutzfeld diseaseC0022336
- Jakob Creutzfeldt DiseaseC0022336
- Jakob Creutzfeldt SyndromeC0022336
- Jakob-Creutzfeldt DiseaseC0022336
- Jakob-Creutzfeldt SyndromeC0022336
- Jakob-Creutzfeldt diseaseC0022336
- Jakob-Creutzfeldt disease (disorder)C0022336
- Jakob-Creutzfeldt disease, unspecifiedC0022336
- SPONGIFORM ENCEPH SUBACUTEC0022336
- Spongiform Encephalopathies, SubacuteC0022336
- Spongiform Encephalopathy, SubacuteC0022336
- Subacute Spongiform EncephalopathiesC0022336
- Subacute Spongiform EncephalopathyC0022336
- Subacute spongiform encephalopathyC0022336
- Syndrome, Creutzfeldt-JakobC0022336
- Syndrome, Jakob-CreutzfeldtC0022336
- Transmissible virus dementiaC0022336
- cjdC0022336
- creutzfeldt jakob diseaseC0022336
- creutzfeldt jakob syndromeC0022336
- creutzfeldt-jakob diseaseC0022336
- creutzfeldt-jakob syndromeC0022336
- jakob-creutzfeldt diseaseC0022336
- jakob-creutzfeldt syndromeC0022336
Frequently Asked Questions
What is the ICD-10 code for creutzfeldt-jakob disease?
The ICD-10-CM code for creutzfeldt-jakob disease is A81.0. The full clinical description is "Creutzfeldt-Jakob disease". A81.0 is a non-billable header code. Use a more specific child code for billing purposes.
What does ICD-10 code A81.0 mean?
ICD-10-CM code A81.0 represents "Creutzfeldt-Jakob disease". It is classified under Chapter 1: Certain Infectious and Parasitic Diseases and is a non-billable header code. Use a more specific child code for billing purposes.
Is A81.0 a billable code?
No, A81.0 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 3 child codes under A81.0.
What chapter is A81.0 in?
A81.0 is in Chapter 1: Certain Infectious and Parasitic Diseases (codes A00-B99).
What codes cannot be used with A81.0?
A81.0 has Excludes1 notes indicating codes that cannot be used together with it, including: certain localized infections - see body system-related chapters; postpolio syndrome (G14); sequelae of poliomyelitis (B91); and 1 more.
What are the subcategories under A81.0?
A81.0 has 3 child codes, including: A81.00 (Creutzfeldt-Jakob disease, unspecified), A81.01 (Variant Creutzfeldt-Jakob disease), A81.09 (Other Creutzfeldt-Jakob disease).
Are additional codes required with A81.0?
Yes, when using A81.0 you should also code: code to identify resistance to antimicrobial drugs (Z16.-); code, if applicable, to identify:; dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4); dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-); dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3); dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2); dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0); mild neurocognitive disorder due to known physiological condition (F06.7-).
What are the UMLS CUIs for A81.0?
A81.0 is linked to 1 UMLS Concept Unique Identifier: C0022336. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.